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Chapter 9 - Agitation and Aggression in Prader-Willi Syndrome

Published online by Cambridge University Press:  26 May 2022

By
Deepan Singh
Edited by
Deepan Singh
Deepan Singh
Affiliation:
Maimonides Medical Center in Brooklyn
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Summary

Agitation and aggression are common behavioral manifestations in patients with PWS. This chapter reviews how to recognize possible triggers and psychological mechanisms behind them. Caregivers are made aware of operant conditioning and the stages of moral development. Additionally the role of externalization is described. The underlying cause of the agitation can vary from person to person and similarly the management strategy differs considerably. The importance of ensuring the safety of the patient and others is emphasized. Behavioral management techniques can be very effective when started at an early age. Medications are effective options to supplement behavioral strategies as long as they are prescribed under the close monitoring of a medical provider. Finally, remember that most patients with PWS do not have malicious intent when they are exhibiting aggression. Their aggression is rooted in poor impulse control and hence is reactive in nature. Their aggression should be treated as a symptom rather than an inherent character flaw.

Keywords

agitationirritabilityaggressiontriggersoperant conditioningmoral developmentexternalizationimpulse controlreinforcement
Type
Chapter
Information
Neuro-behavioral Manifestations of Prader-Willi Syndrome
A Guide for Clinicians and Caregivers
 , pp. 77 - 89
Publisher: Cambridge University Press
Print publication year: 2022

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