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Chapter 39 - Treatment of Focal Hand Dystonia

Published online by Cambridge University Press:  02 November 2023

By
Barbara Illowsky Karp ,
Chandi Prasad Das ,
Daniel Truong  and
Mark Hallett
Edited by
Daniel Truong ,
Dirk Dressler ,
Mark Hallett ,
Christopher Zachary  and
Mayank Pathak
Daniel Truong
Affiliation:
University of California, Riverside
Dirk Dressler
Affiliation:
Hannover Medical School
Mark Hallett
Affiliation:
National Institutes of Health (NIH)
Christopher Zachary
Affiliation:
University of California, Irvine
Mayank Pathak
Affiliation:
Truong Neuroscience Institute
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Summary

Focal hand dystonia (FHD) is characterized by dystonic hand contractions that are often aggravated by purposeful actions and may be specific to a particular task. The term “occupational dystonia” is used when dystonia affecting performance of the job arises in individuals with a particular occupation, usually an occupation requiring repetitive and excessive fine motor activity.

One task-specific FHD, writer’s cramp, causes disabling spasms of the hands when attempting to write, and is particularly likely in people whose profession involves excessive writing. Musician’s dystonia (cramp) is applied to a focal dystonia localized to hand muscles controlling fine movements of the digits or the embouchure muscles involved in playing instruments.

Injection of botulinum neurotoxin (BoNT) is effective in writer’s cramp and other occupational dystonias. This chapter discusses the different common patterns of dystonic movement of the hand and arm, identifies the particular muscles active in each dystonia pattern to aid in target selectio, and illustrates the muscular anatomy and injection approach using anatomical diagrams. Guidance of injections with EMG is discussed. Dosing recommendations for three different BoNT formulations are tabulated.

Keywords

Focal hand dystoniaoccupational dystoiniamovement disorderwriter’s crampmusician’s dystoniayipsbotulinum neurotoxinabobotulinumtoxinABoNT
Type
Chapter
Information
Manual of Botulinum Toxin Therapy , pp. 332 - 347
Publisher: Cambridge University Press
Print publication year: 2023

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