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Chapter 15 - Intestinal Failure Associated Liver Disease

from Section II - Cholestatic Liver Disease

Published online by Cambridge University Press:  19 January 2021

By
Jason Soden  and
Ronald J. Sokol
Edited by
Frederick J. Suchy ,
Ronald J. Sokol  and
William F. Balistreri
Edited in association with
Jorge A. Bezerra ,
Cara L. Mack  and
Benjamin L. Shneider
Frederick J. Suchy
Affiliation:
University of Colorado, Children’s Hospital Colorado, Aurora
Ronald J. Sokol
Affiliation:
University of Colorado, Children’s Hospital Colorado, Aurora
William F. Balistreri
Affiliation:
Cincinnati Children’s Hospital Medical Center, Cincinnati
Jorge A. Bezerra
Affiliation:
Cincinnati Children’s Hospital Medical Center, Cincinnati
Cara L. Mack
Affiliation:
University of Colorado, Children’s Hospital Colorado, Aurora
Benjamin L. Shneider
Affiliation:
Texas Children’s Hospital, Houston
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Summary

Intestinal failure (IF) is defined as the end result of any gastrointestinal disorder in which functional intestinal mass is insufficient to allow adequate growth, hydration, and electrolyte balance in children and adults. Inherent in this definition is the requirement for parental nutrition (PN), which is provided to maintain fluid, energy, protein, electrolyte, and micronutrient delivery in the absence of adequate intestinal function. In the pediatric population, IF may be the end result of various primary etiologies, although the most common is short bowel syndrome (SBS) following congenital or acquired disorders, including necrotizing enterocolitis (NEC), small intestinal atresia, volvulus, and gastroschisis. Table 15.1 summarizes the most common etiologies of pediatric IF.

Type
Chapter
Information
Liver Disease in Children , pp. 242 - 254
Publisher: Cambridge University Press
Print publication year: 2021

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References

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Websites for Further Information

Oley Foundation: https://oley.org/default.aspx

American Society for Parenteral and Enteral Nutrition: www.nutritioncare.org/

Short Bowel Syndrome Foundation: http://shortbowelfoundation.org/

GI Kids (NASPGHAN Foundation): https://gikids.org/digestive-topics/short-bowel-syndrome/

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