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Chapter 18 - Hypertrophic Cardiomyopathy

from Section 3 - Left-Sided Obstructive Lesions

Published online by Cambridge University Press:  09 September 2021

By
Bridget Pearce
Edited by
Laura K. Berenstain  and
James P. Spaeth
Laura K. Berenstain
Affiliation:
Cincinnati Children's Hospital Medical Center
James P. Spaeth
Affiliation:
Cincinnati Children's Hospital Medical Center
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Summary

Hypertrophic cardiomyopathy is a common, autosomal dominant cardiac disease with heterogeneity of expression. Although predominantly an obstructive lesion, it is also characterized by dysrhythmias, diastolic dysfunction, and subendocardial ischemia. Knowledge of the pathophysiology of the disease is imperative in order to provide safe anesthetic care. A comprehensive preoperative evaluation is important in identifying high-risk patients with more malignant forms of the disease. This chapter reviews the abnormalities associated with hypertrophic cardiomyopathy. In addition, strategies to maintain normal sinus rhythm and blood pressure and to prevent catecholamine surges are discussed with specific reference to anesthetic agents and their effects in patients with hypertrophic cardiomyopathy.

Keywords

anesthetic considerationshypertrophic cardiomyopathyhypertrophic obstructive cardiomyopathypediatricpreoperative evaluation
Type
Chapter
Information
Congenital Cardiac Anesthesia
A Case-based Approach
 , pp. 113 - 120
Publisher: Cambridge University Press
Print publication year: 2021

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References

References

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Norrish, B., Forshaw, N., Woo, C., et al. Outcomes following general anesthesia in children with hypertrophic cardiomyopathy. Arch Dis Child 2019; 104: 471–5.CrossRefGoogle ScholarPubMed
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Suggested Reading

Dhillon, A., Khanna, A., Randhawa, M. S., et al. Perioperative outcomes of patients with hypertrophic cardiomyopathy undergoing non-cardiac surgery. Heart 2016; 102: 1627–32.Google Scholar
Norrish, B., Forshaw, N., Woo, C., et al. Outcomes following general anesthesia in children with hypertrophic cardiomyopathy. Arch Dis Child 2019; 104: 471–75.CrossRefGoogle ScholarPubMed

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