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Chapter 7 - Analytic Description of Congenitally Malformed Hearts

Published online by Cambridge University Press:  10 April 2024

Robert H. Anderson
Affiliation:
Institute of Genetic Medicine, Newcastle University
Andrew C. Cook
Affiliation:
University College London
Diane E. Spicer
Affiliation:
University of Florida
Anthony M. Hlavacek
Affiliation:
Medical University of South Carolina
Carl L. Backer
Affiliation:
Cincinnati Children's Hospital
Justin T. Tretter
Affiliation:
Cleveland Clinic, Ohio
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Summary

Systems for describing congenital cardiac malformations have frequently been based on embryological concepts and theories. As useful as these systems have been, they have often had the effect of confusing the clinician, rather than clarifying the basic anatomy of a given lesion. As far as the surgeon is concerned, the essence of a particular malformation lies not in its presumed morphogenesis, but in the underlying anatomy. An effective system for describing this anatomy must be based on the morphology as it is observed. At the same time, it must be capable of accounting for all congenital cardiac conditions, even those that, as yet, might not have been encountered. To be useful clinically, the system must be not only broad and accurate, but also clear and consistent. The terminology used, therefore, should be unambiguous. It should be as simple as possible. The sequential segmental approach provides such a system.1

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Publisher: Cambridge University Press
Print publication year: 2024

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References

References Cited

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