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Ventriculocoronary connection with mitral stenosis/aortic stenosis hypoplastic left heart: a case report

Published online by Cambridge University Press:  30 September 2024

John Karpuk Open the ORCID record for John Karpuk [Opens in a new window] ,
Gabriel Solorzano  and
Jess Randall
John Karpuk*
Affiliation:
Department of Pediatrics, Bernard and Millie Duker Children’s Hospital at Albany Medical Center, Albany, NY, USA
Gabriel Solorzano
Affiliation:
Department of Pediatrics, Bernard and Millie Duker Children’s Hospital at Albany Medical Center, Albany, NY, USA
Jess Randall
Affiliation:
Department of Pediatric Cardiology, Bernard and Millie Duker Children’s Hospital at Albany Medical Center, Albany, NY, USA
*
Corresponding author: John Karpuk; Email: [email protected]
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Abstract

Ventriculocoronary connections develop most commonly in children with mitral stenosis/aortic atresia hypoplastic left heart. These connections can lead to myocardial ischaemia and dysfunction. We report a newborn with mitral stenosis/aortic stenosis hypoplastic left heart who endured systemic ventricular injury post-Norwood, secondary to a large ventriculocoronary fistula. He was treated medically and had favourable outcomes following bidirectional Glenn procedure.

Keywords

Hypoplastic left heartnorwoodmyocardial injurycoronary stealventriculocoronary connectionCHD
Type
Brief Report
Information
Cardiology in the Young , Volume 34 , Issue 9 , September 2024 , pp. 2052 - 2054
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Copyright
© The Author(s), 2024. Published by Cambridge University Press

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