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Transcatheter closure of Abernethy malformation associated with interrupted inferior caval vein and other systemic venous anomalies

Published online by Cambridge University Press:  29 July 2021

Samir Shakya Open the ORCID record for Samir Shakya [Opens in a new window] ,
Anita Saxena  and
Sivasubramanian Ramakrishnan
Samir Shakya
Affiliation:
Pediatric Cardiology, Department of Cardiology, All India Institute of Medical Sciences, New Delhi110029, India
Anita Saxena*
Affiliation:
Department of Cardiology, All India Institute of Medical Sciences, New Delhi110029, India
Sivasubramanian Ramakrishnan
Affiliation:
Department of Cardiology, All India Institute of Medical Sciences, New Delhi110029, India
*
Author for correspondence: Dr A. Saxena, MD, DM, Department of Cardiology, All India Institute of Medical Sciences, Ansari Nagar, New Delhi 110029, India. Tel: +91 01126594861. E-mail: [email protected]
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Abstract

Abernethy malformation is a rare entity. We report a 5-year-old boy presenting with severe pulmonary hypertension in whom Abernethy malformation and inferior caval vein interruption were diagnosed by CT angiography. In addition, the iliac veins were thrombosed with multiple venous collateral drainage. This abnormal venous anatomy caused difficulty in device closure of the Abernethy malformation, which was successfully closed using a vascular plug.

Keywords

Abernethy malformationinferior caval vein interruptiondevice closure
Type
Brief Report
Information
Cardiology in the Young , Volume 32 , Issue 2 , February 2022 , pp. 337 - 339
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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References

Morgan, G, Superina, R. Congenital absence of the portal vein: two cases and a proposed classification system for portasystemic vascular anomalies. J Pediatr Surg 1994; 29: 1239–1241. DOI 10.1016/0022-3468(94)90812-5.10.1016/0022-3468(94)90812-5CrossRefGoogle Scholar
Azad, S, Arya, A, Sitaraman, R, Garg, A. Abernethy malformation: our experience from a tertiary cardiac care center and review of literature. Ann Pediatr Cardiol 2019; 12: 240–247. DOI 10.4103/apc.APC_185_18.CrossRefGoogle ScholarPubMed
Xie, L, Li, Y, Jiang, X, Zhao, J, Xiao, T. A 10-year-old boy with dyspnea and hypoxia: abernathy malformation masquerading as pulmonary arteriovenous fistula. BMC Pediatr 2019; 19: 55. DOI 10.1186/s12887-019-1422-x.CrossRefGoogle ScholarPubMed
Sheth, R, Sivakumar, K. The Abernethy malformation with inferior caval vein hypoplasia: a tailored technique for transcatheter closure and an insight into embryological perspective. Cardiol Young 2018; 28: 1169–1171. DOI 10.1017/S1047951118000884.CrossRefGoogle Scholar
McElhinney, DB, Marx, GR, Newburger, JW. Congenital portosystemic venous connections and other abdominal venous abnormalities in patients with polysplenia and functionally univentricular heart disease: a case series and literature review. Congenit Heart Dis 2011; 6: 28–40. DOI 10.1111/j.1747-0803.2010.00478.x.CrossRefGoogle ScholarPubMed
van der Horst, RL, Hastreiter, AR. Congenital interruption of the inferior vena cava. Chest 1981; 80: 638–640. DOI 10.1378/chest.80.5.638.CrossRefGoogle ScholarPubMed
Venkateshwaran, S, Krishnamoorthy, KM, Sivasankaran, S. Percutaneous device closure of abernethy malformation-a treatable cause of hepatopulmonary syndrome. Catheter Cardiovasc Interv 2014; 83: 968–970. DOI 10.1002/ccd.25275.CrossRefGoogle ScholarPubMed

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