Hostname: page-component-f554764f5-68cz6 Total loading time: 0 Render date: 2025-04-23T00:15:06.885Z Has data issue: false hasContentIssue false
  • English
  • Français

Staged ventricular recruitment following single-ventricular palliation in unbalanced atrioventricular septal defect with heterotaxy syndrome

Published online by Cambridge University Press:  18 October 2024

Somin Im Open the ORCID record for Somin Im [Opens in a new window] ,
Jae Gun Kwak  and
Woong-Han Kim Open the ORCID record for Woong-Han Kim [Opens in a new window]
Somin Im
Affiliation:
Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine, Seoul, Republic of Korea
Jae Gun Kwak
Affiliation:
Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine, Seoul, Republic of Korea
Woong-Han Kim*
Affiliation:
Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine, Seoul, Republic of Korea
*
Corresponding author: Woong-Han Kim; Email: woonghan@snu.ac.kr
Get access Rights & Permissions [Opens in a new window]

Abstract

A newborn with unbalanced atrioventricular septal defect and heterotaxy syndrome underwent early surgeries for single-ventricular palliation due to a small left ventricle. Following procedures, including the modified Damus–Kaye–Stansel, there was a notable increase in left ventricular size. This progression allowed successful biventricular repair at 7 months. This case highlights potential ventricular development after palliative procedures in patients with borderline ventricular size.

Keywords

Unbalanced atrioventricular septal defectbiventricular repairsingle-ventricular palliationDamus–Kaye–Stansel procedure
Type
Brief Report
Information
Cardiology in the Young , Volume 34 , Issue 11 , November 2024 , pp. 2474 - 2476
Check for updates
Copyright
© The Author(s), 2024. Published by Cambridge University Press

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

Article purchase

Temporarily unavailable

References

Cohen, MS, Spray, TL. Surgical management of unbalanced atrioventricular canal defect. Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2005; 8: 135–144.CrossRefGoogle Scholar
Owens, GE, Gomez-Fifer, C, Gelehrter, S, et al. Outcomes for patients with unbalanced atrioventricular septal defects. Pediatr Cardiol 2009; 30: 431–435.CrossRefGoogle ScholarPubMed
Lim, HG, Kim, WA, Lee, YT, et al. Staged biventricular repair of taussig-bing anomaly with subaortic stenosis and coarctation of aorta. Ann Thorac Surg 2003; 76: 1283–1286.CrossRefGoogle ScholarPubMed
Gallo, P, Formigari, R, Hokayem, NJ, et al. Left ventricular outflow tract obstruction in atrioventricular septal defects: a pathologic and morphometric evaluation. Clin Cardiol 1991; 14: 513–521.CrossRefGoogle ScholarPubMed
van Son, JA, Phoon, CK, Silverman, NH, et al. Predicting feasibility of biventricular repair of right-dominant unbalanced atrioventricular canal. Ann Thorac Surg 1997; 63: 1657–1663.CrossRefGoogle ScholarPubMed
Cohen, MS, Jacobs, ML, Weinberg, PM, et al. Morphometric analysis of unbalanced common atrioventricular canal using two-dimensional echocardiography. J Am Coll Cardiol 1996; 28: 1017–1023.CrossRefGoogle ScholarPubMed