Hostname: page-component-586b7cd67f-vdxz6 Total loading time: 0 Render date: 2024-11-22T07:39:38.807Z Has data issue: false hasContentIssue false

Prion disease

Published online by Cambridge University Press:  03 January 2018

Simon Fleminger*
Affiliation:
Department of Psychological Medicine, St Bartholomew's and the Royal London School of Medicine and Dentistry, Turner Street, London
David Curtis
Affiliation:
Department of Psychological Medicine, St Bartholomew's and the Royal London School of Medicine and Dentistry, Turner Street, London
*
Dr Simon Fleminger, The Maudsley Hospital, Denmark Hill, London SE5 8AZ
Rights & Permissions [Opens in a new window]

Abstract

Image of the first page of this content. For PDF version, please use the ‘Save PDF’ preceeding this image.'
Type
Editorials
Copyright
Copyright © 1997 The Royal College of Psychiatrists 

References

Bell, J. E. & Ironside, J. W. (1993) Neuropathology of spongiform encephalopathies in humans. British Medical Bulletin. 49, 738777.Google Scholar
Brown, P., Rodgers-Johnson, P., Cathala, F., et al (1984) Creutzfeldt-Jakob disease of long duration: Clinicopathological characteristics, transmissibility and differential diagnosis. Annals of Neurology, 16, 295304.CrossRefGoogle ScholarPubMed
Brown, P., Rodgers-Johnson, P., Cathala, F., Labouge, R., et al (1985) Epidemiologic implications of Creutzfeldt-Jakob disease in a 19 year old girl. European Journal of Epidemiology 1, 4247.CrossRefGoogle Scholar
Brown, P., Rodgers-Johnson, P., Cathala, F., Labouge, R., Coker-Vann, M., Pomeroy, K., et al (1986) Diagnosis of Creutzfeldt-Jakob disease by Western blot identification of marker protein in human brain tissue. New England Journal of Medicine, 314, 547551.Google Scholar
Brown, P., Rodgers-Johnson, P., Cathala, F., Labouge, R., Coker-Vann, M., Pomeroy, K., Kaur, P., Sulima, M. P., et al (1991) Real and imagined clinicopathological limits of ‘prion dementia’. Lancet, 341, 127129.Google Scholar
Bruce, M., Chree, A., McConnell, I., et al (1994) Transmission of bovine spongiform encephalopathy and scrapie to mice-strain variation and the species barrier. Philosophical Transactions of the Royal Society of London, Series B: Biological Sciences, 343, 405411.Google ScholarPubMed
Büeler, H., Fischer, M., Lang, Y., et al (1992) The neuronal cell surface protein PrP is not essential for normal development and behaviour of the mouse. Nature. 356, 577582.Google Scholar
Cohen, F. E., Pan, K. M., Huang, Z., et al (1994) Structural clues to prion replication. Science, 244, 530531.CrossRefGoogle Scholar
Collinge, J., Owen, F., Poulter, M., et al (1990) Prion dementia without characteristic pathology Lancet. 336, 79.Google Scholar
Collinge, J., Owen, F., Poulter, M., Whittington, M. A., Sidle, K. C., et al (1994) Prion protein is necessary for normal synaptic function. Nature. 370, 295297.CrossRefGoogle ScholarPubMed
Harrison, P. J. & Roborts, G. W. (1991) “Life, Jim, but not as we know it”? Transmissible dementias and the prion protein. British Journal of Psychiatry, 158, 457470.Google Scholar
Halao, K., Baloer, H. F., Crow, T. J., et al (1989) Linkage of a prion protein missence variant to Gerstmann-Sträussler syndrome. Nature, 338, 342345.Google Scholar
Kitamoto, T., Shin, R. W., Doh-Ura, K., et al (1992) Abnormal isoform of prion proteins accumulates in the synaptic structures of the central nervous system in patients with Creutzfeldt-Jakob disease. American Journal of Pathology, 140, 12851294.Google ScholarPubMed
Kulczycki, J., Jedrzajowska, H., Gajkowski, K., et al (1991) Creutzfeldt- Jakob disease in young people. European Journal of Epidemiology, 7, 501504.CrossRefGoogle ScholarPubMed
Monreal, J., Collins, G. H., Masters, C. L., et al (1981) Creutzfeldt-Jakob disease in an adolescent. Journal of Neurological Sciences, 52, 341350.Google Scholar
Packar, R. J., Cornbiath, D. R., Gonatas, N. K., et al (1980) Creutzfeldt-Jakob disease in a 20-year-old woman. Neurology, 381, 492496.Google Scholar
Prusiner, S. B. (1982) Novel proteinaceous infectious particles cause scrapie. Science, 214, 136144.Google Scholar
Prusiner, S. B. & Hsiao, K. K. (1994) Human prion diseases. Annals of Neurology, 35, 385395.Google Scholar
Prusiner, S. B. & Hsiao, K. K., Gajdusek, D. C. & Alpers, M. P. (1982) Kuru with incubation periods exceeding two decades. Annals of Neurology, 12, 19.Google Scholar
Serben, D., Taraboulos, A., DeArmond, S. J., et al (1990) Rapid detection of Creutzfeldt-Jakob disease and scrapie prion proteins. Neurology, 40, 110117.Google Scholar
Will, R. G. (1993) Epidemiology of Creutzfeldt-Jakob disease. British Medical Bulletin, 49, 960970.Google Scholar
Will, R. G. & Mathews, W. B. (1984) A retrospective study of Creutzfeldt-Jakob disease in England and Wales 1970–79 I: Clinical features, Journal of Neurology Neurosurgery and Psychiatry, 47, 134140.CrossRefGoogle ScholarPubMed
Will, R. G. & Mathews, W. B., Ironside, J. W., Zeidler, M., et al (1994) A new variant of Creutzfeldt-Jakob disease in the UK. Lancet, 347, 921925.Google Scholar
Submit a response

eLetters

No eLetters have been published for this article.