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Two Cases of the Sturge-Weber Syndrome

Published online by Cambridge University Press:  29 January 2018

Ranan Rimon  and
Olavi Katila
Ranan Rimon
Affiliation:
University Psychiatric Clinic, Kupittaan Sairaala, Turku Hesperia Hospital, Helsinki, Finland
Olavi Katila
Affiliation:
Neurological Department, Hesperia Hospital, Helsinki, Finland
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Extract

The Sturge-Weber syndrome belongs to the relatively uncommon group of ailments known as heredodegenerative disorders. In 1879 Sturge described a case of epilepsy in a young girl who exhibited a congenital glaucoma and a facial angioma or naevus flammeus. Sturge speculated that the patient's convulsions were caused by a similar naevus formation in the brain. Kalischer (1897, 1901) discovered angiomatotic changes in the meninges, and later the typical calcium deposits corresponding to these angio-mata were found in X-ray examinations by Weber (1922), Dimitri (1923), and Krabbe (1934). The appellation of the Sturge-Weber syndrome varies, owing to the number of its investigators. Levison (1953) calls attention to this question of nomenclature.

Type
Research Article
Information
The British Journal of Psychiatry , Volume 112 , Issue 488 , July 1966 , pp. 709 - 711
Copyright
Copyright © Royal College of Psychiatrists, 1966 

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References

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