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Prader-Willi Syndrome and Psychoses

Published online by Cambridge University Press:  02 January 2018

David J. Clarke
David J. Clarke*
Affiliation:
University of Birmingham Department of Psychiatry, Queen Elizabeth Psychiatric Hospital, Birmingham B15 2QZ
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Abstract

Prader-Willi syndrome (PWS) is associated with an insatiable appetite and (often) other maladaptive behaviours (self-injury, sleep disorders, insistence on routines, and temper tantrums). Psychoses are not a recognised feature. Most affected people have a chromosome 15 abnormality (deletion, disomy, structural rearrangement, etc.). Three people with PWS who developed psychotic disorders in early adult life are described. The nature of the psychoses and the significance of the association are discussed.

Type
Brief Reports
Information
The British Journal of Psychiatry , Volume 163 , Issue 5 , November 1993 , pp. 680 - 684
Copyright
Copyright © Royal College of Psychiatrists, 1993 

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