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Energy metabolism in cystic fibrosis

Published online by Cambridge University Press:  28 February 2007

A. O'Rawe
A. O'Rawe
Affiliation:
The Nuffield Department of Child Health, The Queen's University of Belfast, Institute of Clinical Science, Grosvenor Road, Belfast BT12 6BJ
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Abstract

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Type
Symposium on ‘Cystic Fibrosis’
Information
Proceedings of the Nutrition Society , Volume 51 , Issue 2 , August 1992 , pp. 237 - 244
Copyright
Copyright © The Nutrition Society 1992

References

British Paediatric Association Working Party on Cystic Fibrosis (1988). Cystic Fibrosis in the United Kingdom 1977–85: an improving picture. British Medical Journal 297, 1599–1602.CrossRefGoogle Scholar
Buchdahl, R. M., Cox, M., Fulleylove, C., Marchant, J. L., Tomkins, A. M., Brueton, M. J. & Warner, J. O. (1988). Increased resting energy expenditure in cystic fibrosis. Journal of Applied Physiology 64, 1810–1816.CrossRefGoogle ScholarPubMed
Chandra, R. K. (1989). Long term health implications of mode of infant feeding. Nutritional Research 9,1–3.CrossRefGoogle Scholar
Cotton, C. U., Stutts, M. J., Knowles, M. R., Gatzy, J. T. & Boucher, R. C. (1987). Abnormal apical cell membrane in cystic fibrosis respiratory epithelium. An in vitro electrophysiological analysis. Journal of Clinical Investigation 79, 80–85.CrossRefGoogle Scholar
Dodge, J. A. & Yassa, J. G. (1980). Food intake and supplementary feeding programmes. Proceedings of the 9th International Congress on Cystic Fibrosis, pp. 125–136. Toronto: The Imperial Press Ltd.Google Scholar
Elborn, J. S., Norman, D., Rayner, R., Hiller, E. J. & Shale, D. J. (1990). Plasma tumour necrosis factor alpha in cystic fibrosis. Proceedings of the Cystic Fibrosis Research Workers Conference, Warwick, Abstr. 1:9.Google Scholar
Feigal, R. J. & Shapiro, B. L. (1979). Mitochondria1 calcium uptake and oxygen consumption in cystic fibrosis. Nature 278,276–277.CrossRefGoogle Scholar
Greer, R., Shepherd, R., Cleghorn, G., Bowling, F. G. & Holt, T. (1991). Evaluation of growth and changes in body composition following neonatal diagnosis of cystic fibrosis. Journal of Paediatric Gastroenterology and Nutrition 13,52–58.Google ScholarPubMed
Johnston, J. L., Leong, M. S., Checkland, E. G., Zuberbuhler, P. C., Conger, P. R. & Quinney, H. A. (1988). Body fat assessed from body density and estimated from skinfold thickness in normal children with cystic fibrosis. American Journal of Clinical Nutrition 48, 1362–1366.CrossRefGoogle ScholarPubMed
Kartner, N., Hanrahan, J. W. & Jensen, T. J. (1991). Expression of the cystic fibrosis gene in non-epithelial invertebrate cells produces a regulated anion conductance. Cell 64,681–691.CrossRefGoogle ScholarPubMed
Kawashima, Y. & Bell, R. M. (1987). Assembly of the endoplasmic reticulum phospholipid bilayer. Transporters for phosphatidylcholine and metabolites. Journal of Biological Chemistry 262,16495–16502.CrossRefGoogle ScholarPubMed
Knowles, M. R., Stutts, M. J., Yankasas, J. R., Gatzy, T. J. & Boucher, R. C. (1986). Abnormal respiratory epithelial ion transport in cystic fibrosis. Clinical Chest Medicine 7,285–297.CrossRefGoogle ScholarPubMed
Leclercq-Foucart, J., Forget, P. P. & Van Cutsem, J. L. (1987). Lactulose-rhamnose intestinal permeability in children with cystic fibrosis. Journal of Paediatric Gastroenterology and Nutrition 6,66–70.Google ScholarPubMed
Livingstone, M. B. E., Prentice, A. M., Coward, W. A., Ceesay, S. M., Strain, J. J., Nevin, G. B., Barker, M. E. & Hickey, R. J. (1990). Simultaneous measurement of free-living energy expenditure by the doubly labelled water method and heart-rate monitoring. American Journal of Clinical Nutrition 52, 59–65.CrossRefGoogle ScholarPubMed
Lloyd-Still, J. D. (1976). Clinical studies on the effects of malnutrition during infancy on subsequent physical and intellectual development. In Malnutrition and Intellectual Development, pp. 103–159 [Lloyd-Still, J. D., editor]. Lancaster: MTP Press Ltd.Google Scholar
Luder, E., Kattan, M., Thornton, J. C., Koehler, K. M. & Bonforte, R. J. (1989). Efficacy of a non-restricted fat diet in patients with cystic fibrosis. American Journal of Disease of Childhood 143,458–464.Google Scholar
Mearns, M. B. (1980). The heights of CF patients aged 2–9 years allowing for parental height and severity of pulmonary episodes from birth. In Perspectives in Cystic Fibrosis, pp. 262–265 [Sturgess, J. M., editor]. Toronto: The Imperial Press Ltd.Google Scholar
Murphy, J. L., Wooton, S. A., Bond, S. A. & Jackson, A. A. (1991). Energy content of stools in normal healthy controls and patients with cystic fibrosis. Archives of Disease in Childhood 66,495–500.CrossRefGoogle ScholarPubMed
Newby, M. J., Keim, N. L. & Brown, D. L. (1990). Body composition of adult cystic fibrosis patients and control subjects as determined by densitometry, bioelectrical impedance, total-body electrical conductivity, skinfold measurements, and deuterium oxide dilution. American Journal of Clinical Nutrition 52,209–213.CrossRefGoogle ScholarPubMed
O'Rawe, A., McIntosh, I., Dodge, J. A., Brock, D. J. H., Redmond, A. O. B., Ward, R. & Macpherson, A. J. S. (1991). Increased energy expenditure in cystic fibrosis is associated with specific mutations. Clinical Science (In the Press).Google Scholar
Ringe, D. & Petsko, G. A. (1990). CysticFibrosis. A transport problem? Nature 346,312–313.CrossRefGoogle Scholar
Rogiers, V., Dab, I., Michotte, Y., Vercruysse, A., Crokart, R. & Vis, H. L. (1984). Abnormal fatty acid turnover in the phospholipids of the red blood cell membranes of cystic fibrosis patients (in vitro study). Paediatric Research 18, 704–709.CrossRefGoogle ScholarPubMed
Rommens, J. M., Iannuzzi, M. C., Kerem, B.-S., Drumm, M. L., Melmer, G., Dean, M., Rozmahel, R., Cole, J. L., Kennedy, D., Hidaka, N., Zsiga, M., Buchwald, M., Riordan, J. R., Tsui, L.-S. & Collins, F. S. (1989). Identification of the cystic fibrosis gene: chromosome walking and jumping. Science 245, 1059–1065.CrossRefGoogle ScholarPubMed
Shepherd, R. W., Holt, T. L., Greer, R., Cleghorn, G. J. & Thomas, B. J. (1989). Total body potassium in cystic fibrosis. Journal of Paediatric Gastroenterology and Nutrition 9,200–205.Google ScholarPubMed
Shepherd, R. W., Holt, T. L., Vasques-Velasquez, L., Coward, W. A., Prentice, A. & Lucas, A. (1988). Increased energy expenditure in young children with cystic fibrosis. Lancet i, 1300–1303.CrossRefGoogle Scholar
Shepherd, R. W., Thomas, B. J., Bennett, D., Cooksley, W. G. E. & Ward, L. C. (1983). Changes in body composition and muscle protein degradation during nutritional supplementation in nutritionally growth- retarded children with cystic fibrosis. Journal of Paediatric Gastroenterology and Nutrition 2, 439–446.Google ScholarPubMed
Shrimpton, A. E., McIntosh, I. & Brock, D. J. H. (1991). The incidence of different cystic fibrosis mutations in the Scottish population: effects on prenatal diagnosis and genetic counselling. Journal of Medical Genetics (In the Press).CrossRefGoogle ScholarPubMed
Stutts, M. J., Knowles, M. R., Gatzy, J. T. & Boucher, R. C. (1986). Oxygen consumption and ouabain binding sites in cystic fibrosis nasal epithelium. Paediatric Research 20,1316–1320.CrossRefGoogle ScholarPubMed
Swaminatham, R., Chan, E. L. P., Sin, L. Y., King, N. S., Fun, N. S. & Chan, A. Y. S. (1989). The effect of ouabain on metabolic rate in guinea-pigs: estimation of energy cost of sodium pump activity. British Journal of Nutrition 61,467–473.CrossRefGoogle Scholar
Thomas, P. J., Shengbagamurthi, P., Ysern, X. & Pedersen, P. L. (1991). Cystic fibrosis transmembrane conductance regulator. Nucleotide binding to a synthetic peptide. Science 251,555–557.CrossRefGoogle ScholarPubMed
Tremblay, A., Plourde, G., Despres, J. P. & Bouchard, C. (1989). Impact of dietary fat content and fat oxidation on energy intake in humans. American Journal of Clinical Nutrition 49,799–805.CrossRefGoogle ScholarPubMed
Vaisman, N., Pencharz, P. R., Corey, M., Canny, G. J. & Hahn, E. (1987). Energy expenditure of patients with cystic fibrosis. Journal of Paediatrics 111,496–500.CrossRefGoogle ScholarPubMed
Wulbrand, U., Dork, T., Tummler, B. & Krawczak, M. (1991). Genetic determinants in cystic fibrosis. Lancet 337, 623.CrossRefGoogle ScholarPubMed
Yeagle, P. L. (1989). Lipid regulation of cell membrane structure and function. FEBS Journal 3, 1833–1842.Google ScholarPubMed