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Bullous Pemphigoid in an Infant: A Case Report

Published online by Cambridge University Press:  22 June 2018

Oscar Thabouillot*
Affiliation:
Pediatric Emergency Department, Robert Debré Teaching Hospital, Paris, France Bégin Military Teaching Hospital, Saint-Mandé, France
Julien Le Coz
Affiliation:
Pediatric Emergency Department, Robert Debré Teaching Hospital, Paris, France
Nicolas-Charles Roche
Affiliation:
Bégin Military Teaching Hospital, Saint-Mandé, France
*
Correspondence: Oscar Thabouillot Pediatric Emergency Department Robert Debré Teaching Hospital Paris, France E-mail: [email protected]

Abstract

A seven-month-old girl was referred to the emergency department (ED) after a general practitioner suspected Steven-Johnson syndrome. Actually, the diagnosis of bullous pemphigoid (BP) was made based on biopsies; BP is a rare, autoimmune skin disease involving the presence of blisters known as bullae. The child was efficiently treated with topical steroids. This case shows the importance of the ED physician’s prior knowledge of BP so that a differential diagnosis with other autoimmune diseases (dermatosis, pemphigus) can be made.

Thabouillot O, Le Coz J, Roche NC. Bullous pemphigoid in an infant: a case report. Prehosp Disaster Med. 2018;33(4):448–450.

Type
Case Report
Copyright
© World Association for Disaster and Emergency Medicine 2018 

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Footnotes

Conflicts of interest: none

References

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