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Gargoylism (Hurler's Disease): A Neuropathological Report

Published online by Cambridge University Press:  08 February 2018

D. Naidoo
D. Naidoo*
Affiliation:
From the Department of Neuropathology, Institute of Psychiatry, Maudsley Hospital, University of London
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Extract

Hurler's disease is characterized by chondro-dystrophic skeletal changes, corneal opacities, hepatosplenomegaly and mental defect. The skeletal changes are such that the patient presents a large head, grotesque facies, deformed limbs and kyphosis.

Type
Part I.—Original Articles
Information
Journal of Mental Science , Volume 99 , Issue 414 , January 1953 , pp. 74 - 83
Copyright
Copyright © Royal College of Psychiatrists, 1953 

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