Hostname: page-component-78c5997874-94fs2 Total loading time: 0 Render date: 2024-11-20T00:48:01.133Z Has data issue: false hasContentIssue false
  • English
  • Français

Unilateral hearing loss due to a rhabdomyoma in a six-year-old child

Published online by Cambridge University Press:  29 June 2007

J. P. P. M. van Leeuwen ,
M. Pruszczynski ,
H. A. M. Marres ,
J. A. Grotenhuis  and
C. W. R. J. Cremers
J. P. P. M. van Leeuwen*
Affiliation:
Department of Otorhinolaryngology, University Hospital Nijmegen, The Netherlands.
M. Pruszczynski
Affiliation:
Department of Pathology, University Hospital Nijmegen, The Netherlands.
H. A. M. Marres
Affiliation:
Department of Otorhinolaryngology, University Hospital Nijmegen, The Netherlands.
J. A. Grotenhuis
Affiliation:
Department of Neurosurgery, University Hospital Nijmegen, The Netherlands.
C. W. R. J. Cremers
Affiliation:
Department of Otorhinolaryngology, University Hospital Nijmegen, The Netherlands.
*
J. P. P. M. van Leeuwen, Dept of Otorhinolaryngology, University Hospital Nijmegen, P0 Box 9101,6500 HB Nijmegen, The Netherlands. Fax: (80) 540251
Get access Rights & Permissions [Opens in a new window]

Abstract

A case report of a six-year-old child is presented, who had had a unilateral sensorineural hearing loss for several years. Because of impairment in the ABR as well as in the caloric testing a MRI and CT scan were performed. A 17 mm tumour in the cerebellopontine angle (CPA) was detected, which after suboccipital surgery proved to be a rhabdomyoma. This tumour has not been described before in the CPA. Unilateral sensorineural hearing loss should, at all ages, be an indication for further (radiodiagnostic) investigations.

Keywords

RhabdomyomHearing loss, unilateralCerebello-pontine angleChild
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 109 , Issue 12 , December 1995 , pp. 1186 - 1189
Copyright
Copyright © JLO (1984) Limited 1995

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

Agamanolis, D. P., Dasu, S., Krill, C. E. (1986) Tumors of skeletal muscle. Human Pathology 17: 778–795.CrossRefGoogle ScholarPubMed
Batsakis, J. G., Manning, J. T. (1986) Soft tissue tumors: unusual forms. Otolaryngologic Clinics of North America 19: 659–683.CrossRefGoogle ScholarPubMed
Burger, P. C., Scheithauer, B. W. (1994) Tumors of the central nervous system. In Atlas of Tumor Pathology. Armed Forces Institute of Pathology, Washington, pp 302–308.Google Scholar
Crotty, P. L., Nakhleh, R. E., Dehner, L. P. (1993) Juvenile rhabdomyoma: an intermediate form of skeletal muscle tumor in children. Archives of Pathology and Laboratory Medicine 117: 43–47.Google ScholarPubMed
Enzinger, F. M., Weiss, S. W. (1988) Rhabdomyoma. Soft Tissue Tumors. Mosby, St. Louis, pp 433–447.Google Scholar
Everberg, G. (1960) Unilateral anacusis. Clinical, radiological and genetic investigations. Acta Oto-Laryngologica (Stockholm) (suppl) 158: 366–374.Google Scholar
Ferracini, R., Poggi, S., Frank, G. (1992) Meningeal sarcoma with rhabdomyoblastic Differentiation: case report. Neurosurgery 30: 782–785.Google ScholarPubMed
Fix, S. E., Nelson, J., Schochet, S. S. (1989) Focal leptomeningeal rhabdomyomatosis of the posterior fossa. Archives of Pathology and Laboratory Medicine 113: 872–873.Google Scholar
Fu, Y., Perzin, K. H. (1976) Nonepithelial tumors of the nasal cavity, paranasal sinuses and nasopharynx. Cancer 37: 364–376.Google Scholar
Goldman, R. L. (1969) Gliomyosarcoma of the cerebrum. Report of a unique case. American Journal of Clinical Pathology 52: 741–745.CrossRefGoogle ScholarPubMed
Helliwell, T. R., Sissons, M. C. J., Stoney, P. J., Ashworth, M. T. (1988) Immunochemistry and electron microscopy of head and neck rhabdomyoma. Journal of Clinical Pathology 41: 1058–1063.Google Scholar
Hoffman, S. F., Rorke, L. B. (1971) On finding striated muscle in the brain. Journal of Neurology and Psychiatry 34: 761–764.CrossRefGoogle ScholarPubMed
House, J. W., Brackmann, D. E. (1985) Facial nerve grading system. Otolaryngology—Head and Neck Surgery 93: 146–147.Google Scholar
Jakate, S. M., Marsden, H. B., Ingram, L. (1988) Primary rhabdoid tumor of the brain. Virchows Archives 412: 393–397.Google Scholar
Johnson, E. S., Ludwin, S. K. (1984) Rhabdoneuroglial heterotopias of the pontine leptomeninges in trisomy 13. Archives of Pathology and Laboratory Medicine 108: 906–908.Google ScholarPubMed
Kapadia, S. B., Meis, J. M., Frisman, D. M., Ellis, G. L., Heffner, D. K., Hyams, V. J. (1993) Adult rhabdomyoma in the head and neck: a clinicopathologic and immunophenotypic study. Human Pathology 24: 608–617.Google Scholar
Kleihues, P., Burger, P. C., Scheithauer, B. E. (1993) Histological typing of tumors of the central nervous system. WHO international Classification of Tumors, Springer-Verlag, Berlin/Heidelberg, 28–29.Google Scholar
Knowles, D. M. H., Jacobiec, F. (1975) Rhabdomyoma of the orbit. American Journal of Ophthalmology 80: 1011–1018.Google Scholar
Kodet, R., Newton, W. A., Hamoudi, A. B., Asmar, L. (1991) Rhabdomyosarcomas with intermediate-filament inclusions and features of rhabdoid tumors. American Journal of Surgical Pathology 15: 257–267.Google Scholar
Korinthenberg, R., Edel, G., Palm, D., Muller, K. M., Brandt, M., Muller, R. P. (1984) Primary rhabdomyosarcoma of the leptomeninges: clinical, neuroradiological and pathological aspects. Clinical Neurology and Neurosurgery 86: 301–305.CrossRefGoogle Scholar
Marres, H. A. M. (1994) Genetic deafness. Special reference to branchial arch syndromes. Thesis KU Nijmegen, the Netherlands.Google Scholar
Mehta, A. V. (1993) Rhabdomyoma and ventricular pre excitation syndrome. A report of two cases and review of the literature. American Journal of Diseases in Children 147: 669–671.Google Scholar
Nakheh, R. E., Swanson, P. E., Dehner, L. P. (1991) Juvenile (embryonal and alveolar) rhabdomyosarcoma of the head and neck in adults: a clinical, pathological and histochemical study of 12 cases. Cancer 67: 1019–1024.3.0.CO;2-7>CrossRefGoogle Scholar
Parham, D. M., Weeks, D. A., Beckwith, J. B. (1994) The clinicopathological spectrum of putative extrarenal rhabdoid tumors. American Journal of Surgical Pathology 18: 1010–1029.CrossRefGoogle ScholarPubMed
Shemen, L., Spiro, R., Tuazon, R. (1992) Multifocal and adult rhabdomyomas of the head and neck. Head and Neck 14: 395–400.Google Scholar
Solomon, M. P., Tolete-Velcek, F. (1975) Lingual rhabdomyoma (adult variant) in a child. Journal of Pediatric Surgery 14: 91–94.CrossRefGoogle Scholar
Tatatuto, A. L., Molina, H. A., Diez, B., Zuccaro, G., Monges, J. (1985) Primary rhabdomyosarcoma of brain and cerebellum. Report of four cases in infants: an immunohistochemical study. Acta Neuropathologica (Berlin) 66: 98–104.CrossRefGoogle Scholar
Werb, P., Scurry, J., Ostor, A., Fortune, D., Attwood, H. (1992) Survey of congenital tumors in perinatal necropsies. Pathology 24: 247–253.Google Scholar
Zwick, D. L., Livingston, K., Clapp, L., Kosnik, E., Yates, A. (1989) Intracranial trigeminal nerve rhabdomyoma/choristoma in a child: a case report and discussion of possible histogenesis. Human Pathology 20: 390–393.CrossRefGoogle Scholar