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Sudden sensorineural hearing loss in haemoglobin SC disease

Published online by Cambridge University Press:  29 June 2007

M. Ellis Tavin ,
John S. Rubin  and
Fernando J. Camacho
M. Ellis Tavin
Affiliation:
From the Department of Otorhinolaryngology, Albert Einstein College of Medicine, Bronx, NY, USA.
John S. Rubin*
Affiliation:
From the Department of Otorhinolaryngology, Albert Einstein College of Medicine, Bronx, NY, USA.
Fernando J. Camacho
Affiliation:
From the Department of Montefiore Medical Center, Bronx, NY, USA and the Department of Medicine, Section of Hematology, Albert Einstein College of Medicine, Bronx, NY, USA.
*
Dr John S. Rubin, M.D., F.A.C.S., 48 Sagamore Road, Bronxville, New York 10708, USA.
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Abstract

Presented herein is a case report of sudden sensorineural hearing loss in the setting of haemoglobin SC disease. The relationship of the two is rare; the authors have found that this is only the second report in the literature. In this instance, partial exchange transfusions were performed in an attempt to decrease viscosity and improve blood flow. Thereafter, hearing stabilized and then slowly improved. The evidence for the beneficial role of these transfusions in this setting is, at best, circumstantial, but it is theoretically sound and worthy of further study.

Keywords

Hearing loss, sensorineural, suddenHaemoglobin SC disease
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 107 , Issue 9 , September 1993 , pp. 831 - 833
Copyright
Copyright © JLO (1984) Limited 1993

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