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Simultaneous bilateral cochlear implantation in a five-month-old child with Usher syndrome

Published online by Cambridge University Press:  16 July 2015

A A Alsanosi*
Affiliation:
Department of Otolaryngology, King Saud University, Riyadh, Kingdom of Saudi Arabia
*
Address for correspondence: Dr Abdulrahman Alsanosi, Department of Otolaryngology and Head and Neck Surgery, King Saud University, PO Box 245, Riyadh 11411, Kingdom of Saudi Arabia Fax: 00966 1 4775748 E-mail: [email protected]

Abstract

Objective:

To report a rare case of simultaneous bilateral cochlear implantation in a five-month-old child with Usher syndrome.

Method:

Case report.

Results:

A five-month-old boy with Usher syndrome and congenital profound bilateral deafness underwent simultaneous bilateral cochlear implantation. The decision to perform implantation in such a young child was based on his having a supportive family and the desire to foster his audiological development before his vision deteriorated. The subject experienced easily resolvable intra- and post-operative adverse events, and was first fitted with an externally worn audio processor four weeks after implantation. At 14 months of age, his audiological development was age-appropriate.

Conclusion:

Simultaneous bilateral cochlear implantation is possible, and even advisable, in children as young as five months old when performed by an experienced implantation team.

Type
Clinical Records
Copyright
Copyright © JLO (1984) Limited 2015 

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