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Paediatric otogenic cerebral venous sinus thrombosis: a multidisciplinary approach

Published online by Cambridge University Press:  26 October 2021

J D Constable*
Affiliation:
Department of Otolaryngology, Royal Bristol Hospital for Children, University Hospitals Bristol and Weston NHS Foundation Trust, Bristol, UK
D Hajioff
Affiliation:
Department of Otolaryngology, Royal Bristol Hospital for Children, University Hospitals Bristol and Weston NHS Foundation Trust, Bristol, UK
*
Author for correspondence: Mr James D Constable, Department of Otolaryngology, Royal Bristol Hospital for Children, University Hospitals Bristol and Weston NHS Foundation Trust, Upper Maudlin Street, BristolBS2 8BJ, UK E-mail: [email protected]

Abstract

Background

Paediatric otogenic cerebral venous sinus thrombosis is a rare, heterogeneous and life-threatening condition, with possible otological, neurological and ophthalmological sequelae. Its course and outcomes can be widely variable. The publications available often consider individual aspects of paediatric otogenic cerebral venous sinus thrombosis management. The condition itself and the nature of the currently available guidance can lead to uncertainties when holistically managing patients with paediatric otogenic cerebral venous sinus thrombosis.

Objectives

Clear recommendations for the comprehensive assessment and management of paediatric otogenic cerebral venous sinus thrombosis are presented, along with the literature review upon which they are based. Its clinical and radiological assessment are discussed.

Conclusion

A multidisciplinary approach to assessment and management is recommended, inclusive of infectious diseases, ENT surgery, neurology, ophthalmology and haematology. On balance, anticoagulation is recommended for three months. Follow-up imaging is not recommended in the absence of clinical concern. Follow up by ENT surgery, neurology and ophthalmology departments is recommended.

Type
Review Article
Copyright
Copyright © The Author(s), 2021. Published by Cambridge University Press

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Footnotes

Mr J D Constable takes responsibility for the integrity of the content of the paper

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