Hostname: page-component-586b7cd67f-l7hp2 Total loading time: 0 Render date: 2024-11-26T22:05:33.508Z Has data issue: false hasContentIssue false

Nasal haemophilic pseudotumour

Published online by Cambridge University Press:  29 June 2007

P. Raj*
Affiliation:
Department of Otolaryngology, The Queen Elizabeth Hospital, Edgbaston, Birmingham, UK.
J. T. Wilde
Affiliation:
Department of Haematology, The Queen Elizabeth Hospital, Edgbaston, Birmingham, UK.
J. Oliff
Affiliation:
Department of Radiology, The Queen Elizabeth Hospital, Edgbaston, Birmingham, UK.
A. B. Drake-Lee
Affiliation:
Department of Otolaryngology, The Queen Elizabeth Hospital, Edgbaston, Birmingham, UK.
*
Address for correspondence: Mr P. Raj, 44 Humphrey Middlemore Drive, Harborne, Birmingham B17 0JN.

Abstract

Haemophilic pseudotumour or haemophilic cyst is a rare complication of haemophilia, occurring in one to two per cent of individuals with a severe factor VIII or IX deficiency. We report a case of a haemophilic pseudotumour in a hitherto unreported site, the bony nasal pyramid, and believe this case is also unique on account of it having occurred in a patient with mild haemophilia. The diagnosis and treatment of this rare condition is also reviewed.

Type
Clinical Records
Copyright
Copyright © JLO (1984) Limited 1999

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

Ahlberg, A. K. (1975) On the natural history of haemophilic pseudotumour. Journal of Bone and Joint Surgery 57: 11331136.CrossRefGoogle Scholar
Castaneda, V. L., Parmley, R. T., Bozzini, M. (1991) Radiotherapy of pseudotumours of bone in haemophiliacs with circulating inhibitors to factor VIII. American Journal of Haematology 36: 5559.CrossRefGoogle ScholarPubMed
Echternacht, A. P. (1943) Pseudotumour of bone in haemophilia. Radiology 41: 565572.CrossRefGoogle Scholar
Fernandez de Valderrama, J. A., Matthews, J. M. (1965) The haemophilic pseudotumour or haemophilic subperiosteal haematoma. Journal of Bone and Joint Surgery 47: 265265.Google Scholar
Fernandez-Pallazi, F., Rivas, S. (1985) The use of ‘fibrin-seal’ in surgery of coagulation diseases with special reference to cysts and pseudotumours. In Orthopedic Problems in Haemophilia, Symposium. (Dohring, S., Schulitz, K.P. eds.), W. Zuckschwerdt, Munich, pp 170179.Google Scholar
Ghormley, R. K., Clegg, R. S. (1948) Bone and joint changes in haemophilia. With report of cases of so-called haemophilic pseudotumour. Journal of Bone and Joint Surgery 30: 589600.CrossRefGoogle Scholar
Gilbert, M. S. (1975) Haemophilic pseudotumour. In Handbook of Haemophilia. (Brinkhoust, K. M., Hemker, H. C., eds.), Excerpta Medica, Amsterdam, pp 435446.Google Scholar
Gilbert, M. S. (1997) Pseudotumours (haemophilic blood cysts). In Haemophilia (Forbes, C. D., Aledort, L., Madhok, R., eds.), Chapman & Hall, London, pp 123131.Google Scholar
Horton, D. D., Pollay, M., Wilson, D. A., Brandon, F. M., Sexauer, C. L. (1993) Cranial haemophilic pseudotumour -case report. Journal of Neurosurgery 79: 936938.CrossRefGoogle ScholarPubMed
Hussey, H. H. (1975) Haemophilic pseudotumour of bone. Journal of the American Medical Association 232: 10401041.CrossRefGoogle ScholarPubMed
Jensen, P. S., Putman, C. E. (1975) Haemophilic pseudotumour – diagnosis, treatment, and complications. American Journal of Diseases of Children 129: 717719.CrossRefGoogle ScholarPubMed
Konig, F. (1892) Die Gelenkerkrankungen bei Blutern mit besonderer Berucksichtigung der Diagnose. Sammlung Klinische Vortr Chirurgie 36: 233242.Google Scholar
Liu, S. S., White, W. L., Johnson, P. C, Gauntt, C. (1988) Haemophilic pseudotumour of the spinal canal – case report. Journal of Neurosurgery 69: 624627.CrossRefGoogle ScholarPubMed
Meyers, L., Hakami, N. (1985) Pseudotumour of haemophilia in the orbit: the role of radiotherapy in management. American Journal of Haematology 19: 99104.CrossRefGoogle ScholarPubMed
Mulkey, T. F. (1977) Haemophilic pseudotumours of the mandible. Journal of Oral Surgery 35: 561568.Google ScholarPubMed
Muller, J. H. (1942) Uber die Rontgentherapie von sog. Resorptiongeschwulsten bei Hamophilie. Strahlentherapie 72: 281288.Google Scholar
Starker, L. (1918) Knochenusur durch ein hamophiles subperiostales Hamatom. Mitteilungen aus den Grenzgebieten der Medizin und Chirurgie 31: 381415.Google Scholar
Steel, W. M., Duthie, R. B., O'Connor, B. T. (1969) Haemophilic cysts. Report of five cases. Journal of Bone and Joint Surgery 51: 614616.Google ScholarPubMed
Stoneman, D. W., Beierl, C. D. (1975) Pseudotumour of haemophilia in the mandible. Report of a case. Oral Surgery Oral Medicine and Oral Pathology 40: 811815.CrossRefGoogle ScholarPubMed
Voytek, T. M., Ro, J. Y., Edeiken, J., Ayala, A. G. (1995) Fibrous dysplasia and cemento-ossifying fibroma. A histo-logic spectrum. American Journal of Surgical Pathology 19(7): 775781.CrossRefGoogle Scholar
Wenzl, D. J., Tully, R. J., Giangiacomo, J. (1983) Intraosseous haemophilic pseudotumour of the orbit. Journal of Paedia-tric Ophthalmology and Strabismus 20: 109111.CrossRefGoogle ScholarPubMed
Wessler, S., Avioli, L. V. (1968) Changes in surgical management of haemophiliacs. Pseudotumour of the ilium. Journal of the American Medical Association 206: 22922296.CrossRefGoogle ScholarPubMed