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Moebius' syndrome: a report of two cases

Published online by Cambridge University Press:  29 June 2007

Mousa N. Jamal ,
Nabil S. Samara  and
Mohammed T. A. Al-Lozi
Mousa N. Jamal*
Affiliation:
From the Department of Otolaryngology, Faculty of Medicine, University of Jordan, Amman, Jordan.
Nabil S. Samara
Affiliation:
From the Department of Internal Medicine, Faculty of Madicine, University of Jordan, Amman, Jordan.
Mohammed T. A. Al-Lozi
Affiliation:
From the Department of Internal Medicine, Faculty of Madicine, University of Jordan, Amman, Jordan.
*
Mousa N. Jamal, M.D., Assistant Professor, Department of Otolaryngology, Jordan University Hospital, P.O. Box 13046. Amman, Jordan.
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Abstract

Two patients with Moebius' syndrome are described, a brother and a sister. In addition to bilateral congenital facial nerve paralysis, both had deafness, an external deformity of the auricles, and a latent squint. The deafness in both cases was sensorineural in type; although there was paralysis of the motor part of the facial nerve, taste and lacrimation were intact. This report shows that not all components of the facial nerve are always effected in this syndrome.

Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 102 , Issue 4 , April 1988 , pp. 350 - 352
Copyright
Copyright © JLO (1984) Limited 1988

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