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Initial outcomes from universal newborn hearing screening in Avon

Published online by Cambridge University Press:  24 April 2009

R J Sim ,
S Matthew ,
R J Foley  and
P J Robinson
R J Sim*
Affiliation:
Department of Otolaryngology, Dorset County Hospital, Dorchester, UK
S Matthew
Affiliation:
Department of Otolaryngology, Southmead Hospital, Bristol, UK
R J Foley
Affiliation:
Department of Audiology, Bristol Children's Hospital, UK
P J Robinson
Affiliation:
Department of Otolaryngology, Southmead Hospital, Bristol, UK
*
Address for correspondence: Mr R J Sim, Department of Otolaryngology, Dorset County Hospital NHS Foundation Trust, Dorchester DT1 2JY, UK. Fax: 01305 254155 E-mail: [email protected]
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Abstract

Objective:

The Avon Area Health Authority was a first-phase site for introduction of universal newborn screening in the UK. The aims of this study were: to review the programme's results to date; to assess the impact screening would have on other services (e.g. the cochlear implant programme); and to assess the longer term outcome for children identified by the screening programme.

Patients:

All children identified by the Avon universal newborn hearing screening programme between April 2002 and July 2006.

Results:

Fifty-four children with a bilateral hearing impairment of worse than 40 dBHL were identified from a screened population of approximately 44 000. Nine of these children were put forward for cochlear implantation, and seven had been implanted at the time of writing. Thirteen of these children were identified with possible auditory neuropathy or dys-synchrony. All the newborn hearing screening programme criteria assessed were met.

Conclusions:

The screening programme was effective. Some areas may need review in order to optimise patient care.

Keywords

Sensorineural DeafnessChildUnited KingdomMass Screening
Type
Main Articles
Information
The Journal of Laryngology & Otology , Volume 123 , Issue 9 , September 2009 , pp. 982 - 989
Copyright
Copyright © JLO (1984) Limited 2009

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References

1 Fortnum, HM, Summerfield, AQ, Marshall, DH, Davis, AC, Bamford, JM. Prevalence of permanent childhood hearing impairment in the United Kingdom and implications for universal neonatal hearing screening: questionnaire based ascertainment study. BMJ 2001;323:536–40Google Scholar
2 Yoshinaga-Itano, C, Sedey, AL, Coulter, DK, Mehl, AL. Language of early- and later-identified children with hearing loss. Pediatrics 1998;102:1161–71Google Scholar
3 Moeller, MP. Early intervention and language development in children who are deaf and hard of hearing. www.pediatrics.org/cgi/content/full/106/3/e43Google Scholar
4 Fortnum, H, Davis, A. Epidemiology of permanent childhood hearing impairment in Trent Region, 1985–1993. Br J Audiol 1997;31:409–46Google Scholar
5 Maxon, AB, White, KR, Vohr, BR, Behrens, TR. Using transient evoked otoacoustic emissions for neonatal hearing screening. Br J Audiol 1993;27:149–53Google Scholar
6 Davis, A, Bamford, J, Wilson, I, Ramkalawan, T, Forshaw, M, Wright, S. A critical review of the role of neonatal hearing screening in the detection of congenital hearing impairment. Health Technol Assessment 1997;1:1–176Google Scholar
7 Starr, A, Picton, TW, Sininger, Y, Hood, LJ, Berlin, CI. Auditory neuropathy. Brain 1996;119:741–53Google Scholar
8 Wood, D, Wood, H, Griffiths, A, Howarth, I. Teaching and talking with deaf children. In: Gregory, S. Deaf Children and their Families. Cambridge: Cambridge University Press, 1995Google Scholar
9 Cheng, AK, Rubin, HR, Powe, NR, Mellon, NK, Francis, HW, Niparko, JK. Cost-utility analysis of the cochlear implant in children. JAMA 2000;284:850–6Google Scholar
10 Mohr, PE, Feldman, JJ, Dunbar, JL, McConkey-Robbins, A, Niparko, JK, Rittenhouse, RK et al. The societal costs of severe to profound hearing loss in the United States. Int J Technol Assess 2000;16:1120–35Google Scholar
11 Davis, A, Bamford, J, Stevens, J. Performance of neonatal and infant hearing screens: sensitivity and specificity. Br J Audiol 2001;35:3–15CrossRefGoogle Scholar
12 Stevens, JC, Hall, DM, Davis, A, Davies, CM, Dixon, S. The costs of early hearing screening in England and Wales. Arch Dis Child 1998;78:14–19Google Scholar
13 Wessex Universal Hearing Screening Trial Group. Controlled trial of universal neonatal screening for early identification of permanent childhood hearing impairment. Lancet 1998;352:1957–64Google Scholar
14 Davis, A, Yoshinaga-Itano, C, Hind, S. Commentary: universal newborn hearing screening: implications for coordinating and developing services for deaf and hearing impaired children. BMJ 2001;323:541Google Scholar
15 Nikolopoulos, TP, O'Donoghue, GM, Archbold, S. Age at implantation: its importance in pediatric cochlear implantation. Laryngoscope 1999;109:595–9Google Scholar
16 Nikolopoulos, TP, Archbold, SM, O'Donoghue, GM. The development of auditory perception in children following cochlear implantation. Int J Pediatr Otorhinolaryngol 1999;49:189–91Google Scholar
17 O'Donoghue, GM, Nikolopoulos, TP, Archbold, SM. Determinants of speech perception in children after cochlear implantation. Lancet 2000;356:466–8Google Scholar
18 Govaerts, PJ, De Beukelaer, C, Daemers, K, Ceulaer, G, Yperman, M, Somers, T et al. Outcome of cochlear implantation at different ages from 0 to 6 years. Otol Neurotol 2002;23:885–90Google Scholar
19 Schauwers, K, Gillis, S, Daemers, K, De Beukelaer, C, Govaerts, PJ. Cochlear implantation between 5 and 20 months of age: the onset of babbling and the audiologic outcome. Otol Neurotol 2004;25:263–70CrossRefGoogle Scholar
20 Assessment and Management of Auditory Neuropathy/Auditory Dys-synchrony. A Recommended Protocol. In: hearing.screening.nhs.uk/getdata.php?id=9641 [20 March 2009]Google Scholar
21 Sininger, YS. Identification of auditory neuropathy in infants and children. Semin Hear 2002;23:193–200Google Scholar
22 Butinar, D, Zidar, J, Leonardis, L, Popovic, M, Kalaydjieva, L, Angelicheva, D et al. Hereditary auditory, vestibular, motor, and sensory neuropathy in a Slovenian Roma (Gypsy) kindred. Ann Neurol 1999;46:36–44Google Scholar
23 Pagarkar, W, Bitner-Glindzicz, M, Knight, J, Sirimanna, T. Late postnatal onset of hearing loss due to GJB2 mutations.Int J Pediatr Otorhinolaryngol 2006;70:1119–24CrossRefGoogle Scholar
24 Bamford, J, Fortnum, H, Bristow, K, Smith, J, Vamvakas, G, Davies, L et al. Current practice, accuracy, effectiveness and cost-effectiveness of the school entry hearing screen. Health Technol Assess 2007;11:1–169Google Scholar
25 Gardner, P, Oitmaa, E, Messner, A, Hoefsloot, L, Metspalu, A, Schrijver, I. Simultaneous multigene mutation detection in patients with sensorineural hearing loss through a novel diagnostic microarray: a new approach for newborn screening follow-up. Pediatrics 2006;118:985–94Google Scholar