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Congenital cholesteatoma of the infratemporal fossa

Published online by Cambridge University Press:  03 August 2009

Z Chen
Affiliation:
Department of Otolaryngology, First Affiliated Hospital of Nanjing Medical University, Nanjing, China
L Tang
Affiliation:
Department of Radiology, First Affiliated Hospital of Nanjing Medical University, Nanjing, China
H Zhou
Affiliation:
Department of Otolaryngology, First Affiliated Hospital of Nanjing Medical University, Nanjing, China
G Xing*
Affiliation:
Department of Otolaryngology, First Affiliated Hospital of Nanjing Medical University, Nanjing, China
*
Address for correspondence: Mr Guangqian Xing, Department of Otolaryngology, First Affiliated Hospital of Nanjing Medical University, 300 Guangzhou Road, Nanjing 210029, China. Fax: +86 25 86862837 E-mail: [email protected]

Abstract

Objective:

We report an extremely rare case of congenital cholesteatoma of the infratemporal fossa.

Method:

The clinical, radiological and intra-operative findings of the patient are presented.

Results:

A five-year-old girl presented to our hospital with symptoms in the left ear consistent with middle-ear effusion. A congenital cholesteatoma was not suspected until an enlarging mass in the anteroinferior quadrant of the tympanic membrane was observed. Radiological studies revealed that the mass was located largely in the infratemporal fossa, with limited extension into the tympanic cavity. The patient underwent surgical treatment, which confirmed the clinical and radiological findings.

Conclusion:

This patient's clinical, radiological and intra-operative findings strongly suggested the infratemporal fossa as the site of origin of her congenital cholesteatoma.

Type
Clinical Records
Copyright
Copyright © JLO (1984) Limited 2009

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