Hostname: page-component-cd9895bd7-7cvxr Total loading time: 0 Render date: 2024-12-23T17:14:56.547Z Has data issue: false hasContentIssue false
  • English
  • Français

Congenital cholesteatoma of mastoid origin

Published online by Cambridge University Press:  12 October 2007

J H Lee ,
S J Hong ,
C H Park  and
S H Jung
J H Lee*
Affiliation:
Department of Otorhinolaryngology–Head and Neck Surgery, School of Medicine, Hallym University, Chuncheon
S J Hong
Affiliation:
Department of Otorhinolaryngology–Head and Neck Surgery, School of Medicine, Hallym University, Chuncheon
C H Park
Affiliation:
Department of Otorhinolaryngology–Head and Neck Surgery, School of Medicine, Hallym University, Chuncheon
S H Jung
Affiliation:
Department of Otorhinolaryngology–Head and Neck Surgery, Wonju College of Medicine, Yonsei University, Wonju, South Korea
*
Address for correspondence: Dr Jun Ho Lee, Departments of Otorhinolaryngology–Head and Neck, Surgery, Chuncheon Sacred Heart Hospital, School of Medicine, Hallym University, #153, Kyo-Dong, Chuncheon, Kangwon, South Korea. Fax: 82 33 241 2909 E-mail: [email protected]
Get access Rights & Permissions [Opens in a new window]

Abstract

Objective:

We report an extremely rare case of congenital cholesteatoma of mastoid origin.

Case report:

A male patient was admitted with a one-month history of dizziness and headache, plus tinnitus in the right ear. Computed tomography scanning of the temporal bone showed destruction of the posterior wall of the external auditory canal by a lesion of soft tissue density in the right mastoid cavity, and also destruction of the bony plates of the posterior fossa and the sigmoid sinus, and of the mastoid tegmen. During surgery, a huge cholesteatoma sac was observed in the mastoid cavity, containing a large amount of keratinous material. The tegmen mastoideum and the bony plates of the posterior fossa and the sigmoid sinus were also observed to be destroyed. The skin and the tympanic membrane of the external auditory canal were intact, and the middle ear and aditus ad antrum mucosa were normal. The huge cholesteatoma sac was completely excised via a partial translabyrinthine approach, eradicating the superior and posterior semicircular canals.

Conclusion:

This case of congenital cholesteatoma of mastoid origin was diagnosed by clinical examination, radiological evaluation and surgical findings.

Keywords

CholesteatomaMastoidMiddle EarCongenital
Type
Online Only Clinical Record
Information
The Journal of Laryngology & Otology , Volume 121 , Issue 11 , November 2007 , e20
Copyright
Copyright © JLO (1984) Limited 2007

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1Mevio, E, Gorini, E, Sbrocca, M, Artesi, L, Lenzi, A, Lecce, S et al. Congenital cholesteatoma of the mastoid region. Otolaryngol Head Neck Surg 2002;127:346–8CrossRefGoogle ScholarPubMed
2Rashad, U, Hawthorne, M, Kumar, U, Welsh, A. Unusual cases of congenital cholesteatoma of the ear. J Laryngol Otol 1999;113:52–4CrossRefGoogle ScholarPubMed
3Kazahaya, K, Potsic, WP. Congenital cholesteatoma. Curr Opin Otolaryngol Head Neck Surg 2004;12:398–403CrossRefGoogle ScholarPubMed
4Cureoglu, S, Osma, U, Oktay, MF, Nazaroglu, H, Meric, F, Topcu, I. Congenital cholesteatoma of the mastoid region. J Laryngol Otol 2000;114:779–80CrossRefGoogle ScholarPubMed
5Luntz, M, Telischi, F, Bowen, B, Ress, B, Balkany, T. Congenital cholesteatoma isolated to the mastoid. Ann Otol Rhinol Laryngol 1997;106:608–10CrossRefGoogle ScholarPubMed
6Derlacki, EL, Clemis, JD. Congenital cholesteatoma of the middle ear and mastoid. Ann Otol Rhinol Laryngol 1965;74:706–27CrossRefGoogle ScholarPubMed