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Congenital cholesteatoma in identical twins

Published online by Cambridge University Press:  10 December 2012

T Al Balushi ,
J Z Naik  and
M Al Khabori
T Al Balushi*
Affiliation:
Department of Otolaryngology, Head and Neck Surgery and Communication Disorders, Al Nahdha Hospital, Muscat, Sultanate of Oman
J Z Naik
Affiliation:
Department of Otolaryngology, Head and Neck Surgery and Communication Disorders, Al Nahdha Hospital, Muscat, Sultanate of Oman
M Al Khabori
Affiliation:
Department of Otolaryngology, Head and Neck Surgery and Communication Disorders, Al Nahdha Hospital, Muscat, Sultanate of Oman
*
Address for correspondence: Dr Taji Al Balushi, Department of Otolaryngology, Head and Neck Surgery and Communication Disorders, Al Nahdha Hospital, PO Box 937, PC 112, Ruwi, Muscat, Sultanate of Oman Fax: +968 24834440 E-mail: [email protected]
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Abstract

Objective:

We present an extremely rare case of congenital cholesteatoma in identical twins.

Method:

Case report of congenital cholesteatoma in identical twins, and a literature review, are presented.

Results:

Both cases presented to the ENT out-patient clinic, but with different clinical pictures. Both were managed surgically.

Conclusion:

Congenital cholesteatoma presents as a whitish mass in the middle ear, with an intact tympanic membrane. It is a rare entity comprising between 3.7 and 24 per cent of total cholesteatoma cases. The key to its diagnosis is the absence of previous ear infection, ear surgery and local trauma. To our best knowledge, this paper represents the first report in the world literature of congenital cholesteatoma in identical twins.

Keywords

Cholesteatoma, CongenitalTwins, MonozygoticDiagnosis
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 127 , Issue 1 , January 2013 , pp. 67 - 69
Copyright
Copyright © JLO (1984) Limited 2012

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Footnotes

Presented at the 8th Annual Middle East Update in Otolaryngology Meeting, 8–10 May 2011, Dubai, United Arab Emirates

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