Hostname: page-component-cd9895bd7-gbm5v Total loading time: 0 Render date: 2024-12-24T01:59:05.095Z Has data issue: false hasContentIssue false

Rosai—Dorfman disease of the paranasal sinuses

Published online by Cambridge University Press:  29 June 2007

R. T. Gregor*
Affiliation:
Johannesburg
D. Ninnin
Affiliation:
Johannesburg
*
R. T. Gregor, Ph.D., F.R.C.S. Ed., F.A.C.S., Department of Otolaryngology/Head and Neck Surgery, The Netherlands Cancer Institute, Plesmanlaan 121, 1066 CX Amsterdam, The Netherlands. Fax: 31-20-2152554.

Abstract

A 57-year-old man presented with a history of nasal obstruction of five to six years duration. 'Nasal polyps' were removed on several occasions. He had previously had an episode of paraplegia which resolved after the removal of a spinal tumour. Histology from both sites was thought to represent a malignant fibrous histiocytoma. On presentation the patient had computed tomographical (CT) evidence of extensive ethmoidal disease, with threatened intracranial extension. He also had evidence of lung and retroperitoneal disease with pancreas and kidney involvement. The ethmoidal disease was considered potentially lethal and therefore a craniofacial resection was performed. Review of all the histology revealed that the diagnosis was extranodal Rosai–Dorfman disease (sinus histiocytosis). The patient's course is described, and the literature on this disease of unknown aetiology is reviewed.

Type
Clinical Records
Copyright
Copyright © JLO (1984) Limited 1994

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

Carpenter, R. J., Banks, P. M., McDonald, T. J., Sanderson, D. R. (1978) sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman disease): report of a case with respiratory tract involvement. Laryngoscope 88(12): 19631969.Google Scholar
Chan, J., Mak, K. L., Saw, D. (1985) Sinus histiocytosis with massive lymphadenopathy, a report of two cases in Chinese. Pathology 417: 609612.CrossRefGoogle Scholar
Cheesman, A. D., Lund, V. J., Howard, D. J. (1986) Craniofacial resection for tumours of the nasal cavity and paranasal sinuses. Head and Neck Surgery 8: 429435.CrossRefGoogle ScholarPubMed
Eisen, R. N., Backley, P. J., Rosai, J. (1990) Immunophenotypic characterization of sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman disease). Seminars in Diagnostic Pathology 7: 7482.Google ScholarPubMed
Foucer, E., Rosai, J., Dorfman, R. F. (1984) Sinus histiocytosis with massive lymphadenopathy - an analysis of 14 deaths occurring in a patient registry. Cancer 54: 18341840.3.0.CO;2-F>CrossRefGoogle Scholar
Sanchez, R., Rosai, J., Dorfman, R. F. (1977) Sinus histiocytosis with massive lymphadenopathy; an analysis of 113 cases with special emphasis on its extranodal manifestations. Laboratory Investigation 36: 349350.Google Scholar
Tsang, W. Y. W., Chan, J. K. C., Ho, W. K., Yu, H. C., Chow, L. T. C. (1992) Extranodal Rosai-Dorfman disease: an uncommon cause of persistent nodule in the ears. Journal of Laryngology and Otology 106: 249251.CrossRefGoogle Scholar
Wright, D. H., Richards, D. B. (1981) Sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman disease): report of a case with widespread nodal and extranodal dissemination. Histopathology 5(6): 697709.CrossRefGoogle Scholar