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Primitive neuroectodermal tumour of the tongue

Published online by Cambridge University Press:  14 May 2007

I Gunawardena*
Affiliation:
Department of Otolaryngology, Head and Neck Surgery, Wellington Hospital, Wellington, New Zealand
D Kenwright
Affiliation:
Department of Otolaryngology, Head and Neck Surgery, Wellington Hospital, Wellington, New Zealand
N Steventon
Affiliation:
Department of Otolaryngology, Head and Neck Surgery, Wellington Hospital, Wellington, New Zealand
C Ferguson
Affiliation:
Department of Otolaryngology, Head and Neck Surgery, Wellington Hospital, Wellington, New Zealand
*
Address for correspondence: Dr I Gunawardena, Department of Otolaryngology, Head and Neck Surgery, Waikato Hospital, Waikato DHB, Private Bag 3200, Hamilton 2001, New Zealand. E-mail: [email protected]

Abstract

Peripheral primitive neuroectodermal tumours, which belong to the Ewing sarcoma tumour family, are extremely rare. These tumours are highly aggressive and are known to have a poor prognosis. Immunostaining with at least two neural markers and evidence of an abnormal t(11;22)(q24;q12) translocation are hallmark features in this diagnosis. We present the first reported case of peripheral primitive neuroectodermal tumour to occur in the tongue.

Type
Clinical Record
Copyright
Copyright © JLO (1984) Limited 2007

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References

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