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Plexiform neurofibroma of the larynx in a child

Published online by Cambridge University Press:  08 March 2006

Emre A. Yucel
Affiliation:
Department of Otolaryngology, Istanbul University, Faculty of Medicine, Istanbul, Turkey.
Yahya Guldiken
Affiliation:
Department of Otolaryngology, Istanbul University, Faculty of Medicine, Istanbul, Turkey.
Mustafa Ozdemir
Affiliation:
Department of Otolaryngology, Istanbul University, Faculty of Medicine, Istanbul, Turkey.
A. Settar Ozturk
Affiliation:
Department of Pathology, Istanbul University, Faculty of Medicine, Istanbul, Turkey.

Abstract

A case of a female child of six years of age with a plexiform neurofibroma of the larynx caused by von Recklinghausen’s disease is presented. Laryngeal involvement in neurofibromatosis type 1 (NF1) is rare and only 19 paediatric cases have been reported. The tumour was biopsied and lateral pharyngotomy with supraglottic hemilaryngectomy was performed in order to relieve obstructive symptoms. Problems related to this unusual tumour localization are discussed and a review of the literature is presented.

Type
Research Article
Copyright
© Royal Society of Medicine Press Limited 2002

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