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Neurogenic sarcoma of the sinonasal tract

Published online by Cambridge University Press:  29 June 2007

H. B. Hellquist  and
J. Lundgren
H. B. Hellquist*
Affiliation:
Head and Neck Unit, Department of Pathology, Örebro Medical Centre Hospital, Örebro, Linköping, Sweden.
J. Lundgren
Affiliation:
Department of Otolaryngology, University Hospital, Linköping, Sweden.
*
Henrik B. Hellquist, Head and Neck Unit, Department of Pathology, –Örebro Medical Centre Hospital, S-701 85 Örebro, Sweden. Facsimile +46 19 114390.
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Abstract

Five cases of a rare malignant sinonasal tumour of neurofibromatous nature are described. The term neurogenic sarcoma (or malignant peripheral nerve sheath tumour) is advocated instead of malignant schwannoma.

The clinicopathological features of this tumour are described, and the differential diagnosis are discussed. The necessity of using immunohistochemistry in the diagnosis of sinonasal tumours of fibromatous nature is emphasized. The clinical management consists of radical surgery and adjuvant radiotherapy. Clinically there seems to be a high-grade and a low-grade type of sinonasal neurogenic sarcoma, however, this could not be distinguished histologically in the present series.

Keywords

SarcomaneurogenicParanasal sinus neoplasms
Type
Main Articles
Information
The Journal of Laryngology & Otology , Volume 105 , Issue 3 , March 1991 , pp. 186 - 190
Copyright
Copyright © JLO (1984) Limited 1991

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Footnotes

Part of this work was presented at the European Rhinologic Society Meeting, London, June 1990.

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