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High-resolution computed tomography evaluation of congenital aural atresia – how useful is this?

Published online by Cambridge University Press:  20 July 2020

R Gautam ,
J Kumar ,
G S Pradhan ,
J C Passey ,
R Meher  and
A Mehndiratta
R Gautam
Affiliation:
Department of Radiodiagnosis, Maulana Azad Medical College and Associated Lok Nayak, Govind Ballabh Pant Institute of Postgraduate Medical Education and Research (‘GIPMER’), and Guru Nanak Eye Centre (‘GNEC’) Hospitals, New Delhi, Delhi, India
J Kumar*
Affiliation:
Department of Radiodiagnosis, Maulana Azad Medical College and Associated Lok Nayak, Govind Ballabh Pant Institute of Postgraduate Medical Education and Research (‘GIPMER’), and Guru Nanak Eye Centre (‘GNEC’) Hospitals, New Delhi, Delhi, India
G S Pradhan
Affiliation:
Department of Radiodiagnosis, Maulana Azad Medical College and Associated Lok Nayak, Govind Ballabh Pant Institute of Postgraduate Medical Education and Research (‘GIPMER’), and Guru Nanak Eye Centre (‘GNEC’) Hospitals, New Delhi, Delhi, India
J C Passey
Affiliation:
Department of Otorhinolaryngology, Maulana Azad Medical College and Associated Lok Nayak, Govind Ballabh Pant Institute of Postgraduate Medical Education and Research (‘GIPMER’), and Guru Nanak Eye Centre (‘GNEC’) Hospitals, New Delhi, Delhi, India
R Meher
Affiliation:
Department of Otorhinolaryngology, Maulana Azad Medical College and Associated Lok Nayak, Govind Ballabh Pant Institute of Postgraduate Medical Education and Research (‘GIPMER’), and Guru Nanak Eye Centre (‘GNEC’) Hospitals, New Delhi, Delhi, India
A Mehndiratta
Affiliation:
Department of Radiodiagnosis, Maulana Azad Medical College and Associated Lok Nayak, Govind Ballabh Pant Institute of Postgraduate Medical Education and Research (‘GIPMER’), and Guru Nanak Eye Centre (‘GNEC’) Hospitals, New Delhi, Delhi, India
*
Author for correspondence: Dr Jyoti Kumar, Department of Radiodiagnosis, Maulana Azad Medical College and Associated Lok Nayak, GIPMER and GNEC Hospitals, New Delhi, Delhi-110002, India E-mail: [email protected]
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Abstract

Objective

To depict various temporal bone abnormalities on high-resolution computed tomography in congenital aural atresia patients, and correlate these findings with auditory function test results and microtia subgroup.

Methods

Forty patients (56 ears) with congenital malformation of the auricle and/or external auditory canal were evaluated. Auricles were graded according to Marx's classification, divided into subgroups of minor (grades I and II) and major (III and IV) microtia. Other associated anomalies of the external auditory canal, tympanic cavity, ossicular status, oval and round windows, facial nerve, and inner ear were evaluated.

Results

Minor and major microtia were observed in 53.6 and 46.4 per cent of ears respectively. Mean hearing levels were 62.47 and 62.37 dB respectively (p = 0.98). The malleus was the most commonly dysplastic ossicle (73.3 vs 80.8 per cent of ears respectively, p = 0.53). Facial nerve (mastoid segment) abnormalities were associated (p = 0.04) with microtia subgroup (80 vs 100 per cent in minor vs major subgroups).

Conclusion

Microtia grade was not significantly associated with mean hearing levels or other ear malformations, except for external auditory canal and facial nerve (mastoid segment) anomalies. High-resolution computed tomography is essential in congenital aural atresia, before management strategy is decided.

Keywords

MicrotiaTemporal BoneFacial NerveMiddle Ear
Type
Main Articles
Information
The Journal of Laryngology & Otology , Volume 134 , Issue 7 , July 2020 , pp. 610 - 622
Copyright
Copyright © The Author(s), 2020. Published by Cambridge University Press

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Footnotes

Dr J Kumar takes responsibility for the integrity of the content of the paper

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