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Hearing loss due to cranio-metaphysial dysplasia

Published online by Cambridge University Press:  29 June 2007

D. W. Morgan ,
C. Aldren  and
T. J. Hoare
D. W. Morgan*
Affiliation:
London
C. Aldren
Affiliation:
London
T. J. Hoare
Affiliation:
London
*
D. W. Morgan, B.Sc, F.R.C.S., The Royal National Throat, Nose and Ear Hospital, Gray's Inn Road, London WC1X 8DA.
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Abstract

Craniometaphysial dysplasia is a rare cause of conductive hearing loss. It is a genetic disorder of bone due to decreased osteoclastic activity inthe endosteal and periosteal regions of craniofacial and long bones. The characteristic temporal bone abnormalities are attic fixation, abnormallyshaped ossicles and obliterated foramina ovale. Computerised tomography is helpful in predicting operative findings; surgery should be reserved for those with a severe hearing loss.

Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 104 , Issue 10 , October 1990 , pp. 807 - 808
Copyright
Copyright © JLO (1984) Limited 1990

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