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Congenital stapedial suprastructure fixation with normal footplate mobility: case report

Published online by Cambridge University Press:  14 October 2009

J H Lee ,
S H Jung ,
H C Kim ,
C H Park  and
S M Hong
J H Lee*
Affiliation:
Department of Otorhinolaryngology-Head and Neck Surgery, School of Medicine, Hallym University, Chuncheon, South Korea
S H Jung
Affiliation:
Department of Otorhinolaryngology-Head and Neck Surgery, Wonju College of Medicine, Yonsei University, Wonju, South Korea
H C Kim
Affiliation:
Department of Radiology, School of Medicine, Hallym University, Chuncheon, South Korea
C H Park
Affiliation:
Department of Otorhinolaryngology-Head and Neck Surgery, School of Medicine, Hallym University, Chuncheon, South Korea
S M Hong
Affiliation:
Department of Otorhinolaryngology-Head and Neck Surgery, School of Medicine, Hallym University, Chuncheon, South Korea
*
Address for correspondence: Dr J H Lee, Department of Otorhinolaryngology-Head and Neck Surgery, Chuncheon Sacred Heart Hospital, School of Medicine, Hallym University, #153 Kyo-Dong, Chuncheon, Kangwon, South Korea. Fax: 82 33 241 2909 E-mail: [email protected]
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Abstract

Objective:

We report a case of bilateral conductive hearing loss caused by stapedial suprastructure fixation with normal footplate mobility.

Case report:

A 50-year-old woman had suffered hearing loss in both ears since childhood. Exploratory tympanotomy revealed immobility of the stapes due to a bony bridge between the stapedial suprastructure and the fallopian canal. The incus was missing, while the malleus handle was minimally deformed. The mobility of the stapes footplate was normal. Post-operatively, the hearing in the right ear improved both subjectively and audiographically, while that in the left ear did not improve because of footplate subluxation during surgery.

Conclusion:

This is a rare case of congenital stapedial suprastructure fixation with normal footplate mobility. In this patient, development of the second branchial arch was arrested. When performing exploratory tympanotomy for stapedial fixation, one must keep in mind that normal footplate mobility is possible.

Keywords

Middle EarStapesConductive DeafnessCongenital
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 124 , Issue 6 , June 2010 , pp. 680 - 683
Copyright
Copyright © JLO (1984) Limited 2009

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