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Cochlear implants for congenital deformities

Published online by Cambridge University Press:  29 June 2007

P. D. Phelps*
Affiliation:
London
*
Consultant Radiologist, The Royal National Throat, Nose and Ear Hospital, Gray's Inn Road, London WCIX 8DA.

Abstract

There have been few accounts of multi-channel cochlear implants in patients with congenital structural deformities of the inner ear which are associated with severe and sometimes progressive deafness. These malformations can now be recognized easily on 2 plane thin section high resolution CT studies which are mandatory for the pre-implantation assessment. However, no attempt seems to have been made to describe which of these malformations would be suitable for an implant or for which would this procedure be contra-indicated. True Mondini deformity of both the cochlea and dilated vestibular aqueduct type would appear suitable for a multi channel implant, but this type of implant should not be used for a primitive otocyst, severe labyrinthine dysplasia or the characteristic X-linked deformity.

Type
Main Articles
Copyright
Copyright © JLO (1984) Limited 1992

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References

Gantz, B. J., McCabe, B. R.Tyler, R. S. (1988) Use of multichannel cochlear implants in obstructed and obliterated cochleas. Otolaryngology-Head and Neck Surgery, 98, 7281.CrossRefGoogle ScholarPubMed
Harnsberger, H. R., Dart, D. J., Parkin, J. L., Smoker, W. K., Osborn, A. G. (1987) Cochlear implant candidates: Assessment with CT and MR imaging. Radiology, 164, 5357.CrossRefGoogle ScholarPubMed
Jackler, R. K., Luxford, M. M., Schindler, R. A. & McKerrow, W. S. (1987) Cochlear patency problems in cochlear implantation. Laryngoscope, 97, 801805.CrossRefGoogle ScholarPubMed
Mondini, C. (1791) Anatomica surdi nati secto. Bononiensi Scientarium et artium instituto atque academia commentarii. Bonaniae VII, 419428.Google Scholar
Mueller, D. P., Dolan, K. D., Gantz, B. J. (1989) Temporal bone computed tomography in the pre-operative evaluation for cochlear implantation. Annals of Otology, Rhinology & Laryngology, 98, 346349.CrossRefGoogle Scholar
Phelps, P. D. (1986) Congenital cerebrospinal fluid fistulae of the petrous temporal bone. Clinical Otolaryngology, 11, 7992.CrossRefGoogle ScholarPubMed
Phelps, P. D., Lloyd, G. A. S. (1978) Congenital deformity of the internal auditory meatus and labyrinth associated with cerebrospinal fluid fistula. Advances in Oto-Rhino-Laryngology, 24, 5157.CrossRefGoogle ScholarPubMed
Phelps, P. D., Lloyd, G. A. S. (1990) Diagnostic Imaging of the Ear, Springer Verlag, Berlin, p. 43.CrossRefGoogle ScholarPubMed
Phelps, P. D., Annis, J. A. D.Robinson, P. J. (1990) Imaging for cochlear implants. British Journal of Radiology, 63, 512516.CrossRefGoogle ScholarPubMed
Phelps, P. D., Reardon, W., Pembrey, M. E., Bellman, S., Luxon, L. (1991) X-Linked deafness, stapes gushers and a distinctive defect of the inner ear. Neuroradiology, 33, 326330.CrossRefGoogle Scholar
Reardon, W., Middleton-Price, H. R., Sandkuijl, L., Phelps, P. D., Bellman, S., Luxon, L., Pembrey, M. E., Malcolm, S. (1991) A multipedigree linkage study of X-linked deafness: linkage to Xq13-q12 and evidence for genetic heterogenity. Genomics, 11, 885894.CrossRefGoogle Scholar
Shelton, C., Luxford, W. M. M., Tonokawa, L. L., Lo, W. W. M. (1989) The narrow internal auditory canal in children: a contraindication to cochlear implants. Otolaryngology-Head and Neck Surgery, 100, 227231.CrossRefGoogle ScholarPubMed
Silverstein, H., Smouha, E., Morgan, N. (1988) Multichannel cochlear implantation in a patient with bilateral Mondini deformities. American Journal of Otology, 9, 451454.Google Scholar