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Behavioural management of Prader-Willi syndrome

Published online by Cambridge University Press:  13 June 2014

Pat Gibbons  and
Kathryn O'Donoghue
Kathryn O'Donoghue
Affiliation:
Warrenstown house, Blanchardstown, Dublin 15, Ireland.
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Abstract

Prader-Willi syndrome is a genetic illness associated with a defect on chromosome 15. It presents with hypotonicity in infancy followed by voracious appetite and gross obesity from early childhood and with a range of other clinical and behavioural sequelae. This case report is of an adolescent boy who was admitted to a psychiatric unit for an intensive behavioural programme to control his weight gain and deal with associated behavioural problems, and demonstrates that an inpatient programme can lead to sustainable improvements in weight control and other indicators of well-being in PWS patients.

Keywords

Prader-Willi syndromeHyperphagiaObesityBehavioural management.
Type
Case Reports
Information
Irish Journal of Psychological Medicine , Volume 15 , Issue 1 , March 1998 , pp. 32 - 34
Copyright
Copyright © Cambridge University Press 1998

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