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Unguarded tricuspid valvar orifice in the fetus

Published online by Cambridge University Press:  21 January 2005

Kenny K. Wong ,
Duncan I. Farquharson  and
Walter J. Duncan
Kenny K. Wong
Affiliation:
Division of Pediatric Cardiology, British Columbia Children’s and Women’s Hospitals, Vancouver, British Columbia, Canada
Duncan I. Farquharson
Affiliation:
Division of Maternal Fetal Medicine, British Columbia Children’s and Women’s Hospitals, Vancouver, British Columbia, Canada
Walter J. Duncan
Affiliation:
Division of Pediatric Cardiology, British Columbia Children’s and Women’s Hospitals, Vancouver, British Columbia, Canada
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Abstract

The unguarded tricuspid valve is uncommon. We describe herein a fetus with a grossly dilated right ventricle and atrium, with severe tricuspid and pulmonary valvar regurgitation. The right ventricle was akinetic, and no tricuspid tissue or valvar apparatus was identified. Colour Doppler showed a highly unusual retrograde flow of blood through the right heart. The pregnancy was terminated, and necropsy examination confirmed the gross dilation of the right heart chambers, with severely dysplastic valvar tissue at the right atrioventricular junction effectively giving an unguarded orifice. There was no valvar displacement, and the left heart was normal. The fetus had a normal karyotype, albeit with absent kidneys.

Keywords

Dysplastic tricuspid valvefetal echocardiographyright-to-left shunting
Type
Brief Report
Information
Cardiology in the Young , Volume 14 , Issue 5 , October 2004 , pp. 557 - 559
Copyright
© 2004 Cambridge University Press

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References

Kanjuh VI, Stevenson JE, Amplatz K, Edwards JE. Congenitally unguarded tricuspid orifice with coexistent pulmonary atresia. Circulation 1964; 30: 911–917.Google Scholar
Anderson RH, Silverman NH, Zuberbuhler JR. Congenitally unguarded tricuspid orifice: its differentiation from Ebstein’s malformation in association with pulmonary atresia and intact ventricular septum. Pediatr Cardiol 1990; 11: 86–90.Google Scholar
Freedom RM, Culham G, Moes F, Olley PM, Rowe RD. Differentiation of functional and structural pulmonary atresia: Role of aortography. Am J Cardiol 1978; 41: 914–920.Google Scholar
Ozkutlu S, Gunal N, Caglar M, Alehan D, Gungor C. Unguarded tricuspid orifice: a rare malformation of tricuspid valve diagnosed by echocardiography. Report of two cases and review of the literature. Int J Cardiol 1996; 56: 125–129.Google Scholar
Mohan JC, Passey R, Arora R. Unguarded tricuspid orifice and patent right ventricular outflow tract presenting with long-standing severe right heart failure in an adult. Int J Cardiol 1998; 66: 85–87.Google Scholar
Mohan JC, Passey R, Arora R. Echocardiographic spectrum of congenitally unguarded tricuspid valve orifice and patent right ventricular outflow tract. Int J Cardiol 2000; 74: 153–157.Google Scholar
Brili S, Stefanadis C, Toutouzas P. Congenitally unguarded tricuspid orifice associated with underdeveloped pulmonary valve leaflets. Heart 2001; 86: 138.Google Scholar
Mohan JC, Sengupta PP, Arora R. Congenitally unguarded tricuspid valve orifice with a giant right atrium and a massive clot in an asymptomatic adult. Indian Heart J 2001; 53: 503–504.Google Scholar
Hornberger LK, Sahn DJ, Kleinman CS, Copel JA, Reed KL. Tricuspid valve disease with significant tricuspid insufficiency in the fetus: diagnosis and outcome. J Am Coll Cardiol 1991; 17: 167–173.Google Scholar
Shahani R, Magotra RA. Late follow-up of tricuspid valve replacement for unguarded tricuspid annulus. J Thorac Cardiovasc Surg 1996; 112: 555–556.Google Scholar