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Transposition of the great arteries and sinus venosus defect with partially anomalous pulmonary venous return: physiological and anatomic considerations

Published online by Cambridge University Press:  06 June 2014

Vijayakumar Raju ,
Rahul Rathod ,
Luis G. Quinonez  and
Christopher W. Baird
Vijayakumar Raju
Affiliation:
Department of Cardiovascular Surgery, Boston Children Hospital, Harvard Medical School, Boston, Massachusetts, United States of America
Rahul Rathod
Affiliation:
Department of Cardiology, Boston Children Hospital, Harvard Medical School, Boston, Massachusetts, United States of America
Luis G. Quinonez
Affiliation:
Department of Cardiovascular Surgery, Boston Children Hospital, Harvard Medical School, Boston, Massachusetts, United States of America
Christopher W. Baird*
Affiliation:
Department of Cardiovascular Surgery, Boston Children Hospital, Harvard Medical School, Boston, Massachusetts, United States of America
*
Correspondence to: C. W. Baird, Department of Cardiovascular Surgery, Boston Children Hospital, Harvard Medical School, 300 Longwood Avenue, Bader 273, Boston, MA 02115, United States of America. Tel: 617-355-1914; Fax: 617-730-0214; E-mail: [email protected]
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Abstract

Transposition of the great arteries is a common congenital heart defect causing cyanosis in neonates, occurring in 0.2 per 1000 live births. It has been reported to occur with other associated congenital heart lesions. However, its association with a superior sinus venosus defect and partially anomalous pulmonary venous return has not been reported. We present a neonate with transposition of the great arteries, superior sinus venosus defect with partially anomalous pulmonary venous return that underwent successful complete neonatal repair, and discuss important physiological and anatomic considerations.

Keywords

Congenital heart diseasetransposition of the great vesselssinus venosus septal defectpartially anomalous pulmonary venous return
Type
Brief Reports
Information
Cardiology in the Young , Volume 25 , Issue 4 , April 2015 , pp. 787 - 789
Copyright
© Cambridge University Press 2014 

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