Hostname: page-component-78c5997874-4rdpn Total loading time: 0 Render date: 2024-11-05T09:49:49.880Z Has data issue: false hasContentIssue false
  • English
  • Français

Transcatheter management of mid-aortic syndrome secondary to myofibroma presenting in infancy with severe left ventricular dysfunction: a case report

Published online by Cambridge University Press:  08 October 2015

Ryan Callahan ,
Jacqueline Kreutzer  and
Mark Debrunner
Ryan Callahan*
Affiliation:
Department of Cardiology, Boston Children’s Hospital and Harvard Medical School, Boston, Massachusetts, United States of America
Jacqueline Kreutzer
Affiliation:
University of Pittsburgh Medical School, University of Pittsburgh Medical Center, Division of Cardiology, Children’s Hospital of Pittsburgh, Pittsburgh, Pennsylvania, United States of America
Mark Debrunner
Affiliation:
University of Pittsburgh Medical School, University of Pittsburgh Medical Center, Division of Cardiology, Children’s Hospital of Pittsburgh, Pittsburgh, Pennsylvania, United States of America
*
Correspondence to: R. Callahan, MD, Department of Cardiology, Boston Children’s Hospital, 300 Longwood Ave, Boston, MA 02115, United States of America. Tel: +617 355 6529; Fax: +617 730 7548; E-mail: [email protected]
Get access Rights & Permissions [Opens in a new window]

Abstract

In this study, we summarise a case of a myofibroma causing mid-aortic syndrome due to obstruction of the distal thoracic and abdominal aorta leading to severe left ventricular dysfunction. The patient was managed with percutaneous intervention via balloon dilation and stent placement. On follow-up, the patient has normalisation of ventricular function, is off anti-hypertensives, and is being monitored for re-stenosis.

Keywords

Catheterisationmid-aortic syndromemyofibroma
Type
Brief Reports
Information
Cardiology in the Young , Volume 26 , Issue 4 , April 2016 , pp. 799 - 801
Check for updates
Copyright
© Cambridge University Press 2015 

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1. Gopal, M, Chahal, G, Al-Rifai, Z, Eradi, B, Ninan, G, Nour, S. Infantile myofibromatosis. Pediatr Surg Int 2008; 24: 287–291.Google Scholar
2. Oudijk, L, den Bakker, MA, Hop, WC, et al. Solitary, multifocal and generalized myofibromas: clinicopathological and immunohistochemical features of 114 cases. Histopathology 2012; 60: E1–E11.Google Scholar
3. Wiswell, TE, Davis, J, Cunnigham, BE, Solenberger, R, Thomas, PJ. Infantile myofibromatosis: the most common fibrous tumor of infancy. J Pediatr Surg 1988; 23: 315–318.Google Scholar
4. Schurr, P, Moulsdale, W. Infantile myofibroma: a case report and review of the literature. Adv Neonatal Care 2008; 8: 13–20.Google Scholar
5. Sen, PK, Kinare, SG, Engineer, SD, Parulkar, GB. The middle aortic syndrome. Br Heart J 1963; 25: 610–618.Google Scholar
6. Porras, D, Stein, DR, Ferguson, MA, et al. Midaortic syndrome: 30 years of experience with medical, endovascular and surgical management. Pediatr Nephrol 2013; 28: 2023–2033.Google Scholar
7. Tummolo, A, Marks, SD, Stadermann, M, et al. Mid-aortic syndrome: long-term outcome of 36 children. Pediatr Nephrol 2009; 24: 2225–2232.Google Scholar
8. McElhinney, DB, Marshall, AC, Schievano, S. Fracture of cardiovascular stents in patients with congenital heart disease: theoretical and empirical considerations. Circ Cardiovasc Interv 2013; 6: 575–585.CrossRefGoogle ScholarPubMed
9. Sathanandam, SK, Haddad, LM, Subramanian, S, et al. Unzipping of small diameter stents: an in vitro study. Catheter Cardiovasc Interv 2015; 85: 249–258.CrossRefGoogle ScholarPubMed