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Tetralogy of Fallot with pulmonary atresia and aortopulmonary window may mimic common arterial trunk

Part of: Basic Science

Published online by Cambridge University Press:  17 June 2021

Sudesh Prabhu Open the ORCID record for Sudesh Prabhu [Opens in a new window] ,
Manaswini Keshav ,
Prakash Ramachandra ,
Vimal Raj ,
Colin John  and
Tom R Karl
Sudesh Prabhu*
Affiliation:
Paediatric Cardiac Services, Narayana Institute of Cardiac Sciences, Bengaluru, India
Manaswini Keshav
Affiliation:
Medical Student, MS Ramaiah Medical College, Bengaluru, India
Prakash Ramachandra
Affiliation:
Paediatric Cardiac Services, Narayana Institute of Cardiac Sciences, Bengaluru, India
Vimal Raj
Affiliation:
Paediatric Cardiac Services, Narayana Institute of Cardiac Sciences, Bengaluru, India
Colin John
Affiliation:
Paediatric Cardiac Services, Narayana Institute of Cardiac Sciences, Bengaluru, India
Tom R Karl
Affiliation:
Queensland Pediatric Cardiac Research, University of Queensland, Brisbane, Australia
*
Author for correspondence: Sudesh Prabhu, Department of Pediatric Cardiac Surgery, Narayana Institute of Cardiac Sciences, 258/A Hosur Road, Bommasandra Industrial Area, Anekal Taluk, Bengaluru, Karnataka 560099, India. Tel: +919886899450. E-mail: [email protected]
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Abstract

Tetralogy of Fallot with pulmonary atresia is a group of congenital cardiac malformations, which is defined by the absence of luminal continuity between both ventricles and the pulmonary artery, and an interventricular communication. Pulmonary arterial supply in patients with tetralogy of Fallot with pulmonary atresia can be via the arterial duct or from collateral arteries arising directly or indirectly from the aorta (systemic-to-pulmonary artery collaterals), or rarely both. The rarest sources of pulmonary blood flow are aortopulmonary window and fistulous communication with the coronary artery.

Herein, we describe an outflow tract malformation, tetralogy of Fallot with pulmonary atresia and aortopulmonary window, which was misdiagnosed as common arterial trunk. We emphasise the morphological differences.

Keywords

Pulmonary atresiaventricular septal defectaortopulmonary windowcommon arterial trunksub-pulmonary infundibulumpulmonary blood flow
Type
Original Article
Information
Cardiology in the Young , Volume 32 , Issue 3 , March 2022 , pp. 410 - 414
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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