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Surgical correction of a patient with discordant atrioventricular and concordant ventriculo-arterial connections

Published online by Cambridge University Press:  19 August 2008

Kiyozo Morita ,
Hiromi Kurosawa  and
Hisaki Miyamoto
Kiyozo Morita
Affiliation:
Jikei University School of Medicine, Department of Cardiovascular Surgery, Tokyo, Japan
Hiromi Kurosawa*
Affiliation:
Jikei University School of Medicine, Department of Cardiovascular Surgery, Tokyo, Japan
Hisaki Miyamoto
Affiliation:
Jikei University School of Medicine, Department of Cardiovascular Surgery, Tokyo, Japan
*
Hiromi Kurosawa, M.D. Department of Cardiac Surgery, Jikei Univ. School of Medicine, 3-19-18 Nishi-shinbashi, Minato-ku, Tokyo, 105, Japan. Tel 3-3433-1111; Fax: 3-3943-7515
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Abstract

The combination of discordant atrioventricular and concordant ventriculoarterial connections is an extremely rare entity, with only 8 cases of successful surgical repair being previously reported. Although from the clinical standpoint this anomaly is similar to complete transposition, this unusual combination is clearly suited by its morpho-physiological features to an atrial rather than an arterial switch procedure. A 17-year-old boy with this malformation, associated also with severe pulmonary hypertension, underwent a palliative Senning procedure, leaving the ventricular septal defect open and banding the pulmonary trunk. Postoperatively, hypoxemia was markedly improved, and was associated with a reduction of the level of pulmonary hypertension, contributing to marked symptomatic improvement.

Keywords

Senning procedurediscordant atriovencricular and concordant ventriculo-arterial connectionsventricular topology
Type
Brief-Reports
Information
Cardiology in the Young , Volume 7 , Issue 4 , October 1997 , pp. 442 - 445
Copyright
Copyright © Cambridge University Press 1997

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References

1.Van, Praagh R, Van, Praagh S. Isolated ventricular inversion: a consideration of the morphogenesis, definition and diagnosis of nontransposed and transposed great arteries.Am J Cardiology 1966;17:395–406Google Scholar
2.Espino-Vela, J, de, la Cruz MV, Munoz-Castellanos, L, Plaza, L, Attie, F. Ventricular inversion without transposition of the great vessels in situs inversus. British Heart Journal 1970; 32: 292–303.CrossRefGoogle ScholarPubMed
3.Ostermeyer, J, Bircks, W, Krian, A, Sievers, G, Hilgenberg, F. Isolated atrioventricular discordance: report of two surgical cases with isolated ventricular inversion. J Thorac Cardiovasc Surg 1983; 86: 926–929.CrossRefGoogle ScholarPubMed
4.Snider, AR, Enderlein, MA, Teitel, DF, Hirji, M, Heymann, MA. Isolated ventricular inversion: two-dimensional echocardiographic findings and a review of the literature. Pediatr Cardiol 1984; 5: 27–33.CrossRefGoogle Scholar
5.Arciprete, P, Macartney, FJ, deLeval, M, Stark, J. Mustard's operation for patients with ventriculoarterial concordance: report of two cases and a cautionary tale. British Heart Journal 1985; 53: 443–450:CrossRefGoogle Scholar
6.Baudet, EM, Hafez, A, Choussat, A, Roques, X. Isolated ventricular inversion with situs solitus: successful surgical repair. Ann Thorac Surg 1986; 41: 91–94.CrossRefGoogle ScholarPubMed
7.Ranjit, MS, Wilkinson, JL, Mee, RBB. Discordant atrioventricularconnexion withconcordantventriculoarterial connextion (so-called “isolated ventricular inversion”) with usual atrial arrangement (situs solitus). International J Cardiology 1991; 31: 114–117.CrossRefGoogle Scholar
8.Kurosawa, H, Imai, Y, Becker, AE. Congenitally corrected transposition with normally positioned atria, straddling mitral valve, and isolated posterior atrioventricular node and bundle. J Thorac Cardiovasc Surg 1990; 99: 312–313.CrossRefGoogle ScholarPubMed
9.Yamaki, S, tezuka, F. Quantitative analysis of pulmonary vascular disease in complete transposition of the great arteries. Circulation 1976; 54: 805–809.CrossRefGoogle ScholarPubMed
10.Anderson, RH, Wilkinson, JL. Isolated ventricular inversion with situs solitus. British Heart Journal 1975; 37: 1202–1204.CrossRefGoogle ScholarPubMed