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Supravalvar stenosing tricuspid ring in congenitally corrected transposition

Published online by Cambridge University Press:  19 August 2008

Gordon Gladman
Affiliation:
Cardiology and Critical Care Medicine, The Hospital for Sick Children, University of Toronto, Toronto
Frank Casey
Affiliation:
Cardiology and Critical Care Medicine, The Hospital for Sick Children, University of Toronto, Toronto
Ian Adatia*
Affiliation:
Cardiology and Critical Care Medicine, The Hospital for Sick Children, University of Toronto, Toronto
*
Dr. Ian Adatia, Cardiology and Critical Care Medicine, The Hospital for Sick Children, Toronto, Canada, M5G 1X8. Tel. 416-813-6140; Fax. 416-813-7547.

Summary

We report an unusual case with discordant atrioventricular and ventriculoarterial connections. In addition to the commonly associated intracardiac anomalies ofventricular septal defect and subpulmonary tissue tags, a supravalvar ring was present above the left-sided, morphologically tricuspid valve. This case highlights the value of color flow Doppler echocardiography in making the diagnosis, particularly as the supravalvar ring was seen poorly angiographically.

Type
Brief Reports
Copyright
Copyright © Cambridge University Press 1996

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