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Scimitar syndrome associated with absence of the right pulmonary artery and a persistent primitive hepatic venous plexus

Published online by Cambridge University Press:  22 April 2005

Gabriella Agnoletti ,
Damien Bonnet  and
Jacques De Blic
Gabriella Agnoletti
Affiliation:
Service de Cardiologie Pédiatrique, Necker Enfants Malades, Paris, France
Damien Bonnet
Affiliation:
Service de Cardiologie Pédiatrique, Necker Enfants Malades, Paris, France
Jacques De Blic
Affiliation:
Service de Pneumologie Pédiatrique, Necker Enfants Malades, Paris, France
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Abstract

An 18-month-old boy, referred because of an infection of the airways, was found to have a right-sided heart, a hypoplastic right lung, absence of the right pulmonary artery, and persistence of the hepatic venous plexus. The benign association of this unusual variant of the scimitar syndrome and persistence of the hepatic venous plexus needs to be recognised in order to avoid extensive investigations and surgery involving the inferior caval vein.

Keywords

Anomalous pulmonary venous connectionanomalous systemic venous connectioninferior caval vein
Type
Brief Report
Information
Cardiology in the Young , Volume 15 , Issue 2 , March 2005 , pp. 216 - 218
Copyright
© 2005 Cambridge University Press

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References

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