Hostname: page-component-586b7cd67f-rdxmf Total loading time: 0 Render date: 2024-11-26T21:55:04.092Z Has data issue: false hasContentIssue false
  • English
  • Français

Rhabdomyoma of the interventricular septum presenting as a Brugada phenocopy

Published online by Cambridge University Press:  04 May 2011

Timothy Nguyen ,
John Smythe  and
Adrian Baranchuk
Timothy Nguyen
Affiliation:
Division of Cardiology, Kingston General Hospital, Queen's University, Canada
John Smythe
Affiliation:
Division of Cardiology, Kingston General Hospital, Queen's University, Canada
Adrian Baranchuk*
Affiliation:
Division of Cardiology, Kingston General Hospital, Queen's University, Canada
*
Correspondence to: Dr A. Baranchuk, MD FACC, Associate Professor of Medicine, Cardiac Electrophysiology and Pacing, Kingston General Hospital K7L 2V7, Queen's University, Canada. Tel: 613 549 6666 ext 3801; Fax: 613 548 1387; E-mail: [email protected]
Get access Rights & Permissions [Opens in a new window]

Abstract

Brugada syndrome is a channelopathy characterised electrocardiographically by distinctive coved ST-segment elevation in the right precordial leads and is associated with a predisposition for sudden death secondary to ventricular arrhythmias in otherwise healthy patients. Previously known as Brugada-like patterns, Brugada phenocopies include agents and conditions that mimic true Brugada syndrome, presenting with an acquired Brugada Type-1 ECG pattern. We describe the first reported case of a 17-month-old female with an asymptomatic rhabdomyoma of the interventricular septum that presented as a Brugada phenocopy.

Keywords

Brugada syndromeBrugada ECG-like patternintracardiac tumour
Type
Brief Reports
Information
Cardiology in the Young , Volume 21 , Issue 5 , 09 September 2011 , pp. 591 - 594
Copyright
Copyright © Cambridge University Press 2011

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1.Antzelevitch, C, Brugada, P, Borggrefe, M, et al. Brugada syndrome: report of the second consensus conference: endorsed by the heart rhythm society and the European Heart Rhythm Association. Circulation 2005; 111: 659–670.CrossRefGoogle ScholarPubMed
2.Riera, ARP, Uchida, AH, Schapachnik, E, et al. Propofol infusion syndrome and Brugada syndrome electrocardiographic phenocopy. Cardiol J 2010; 17: 130–135.Google Scholar
3.Arce, M, Riera, ARP, Femenia, F, Baranchuk, A. Brugada electrocardiographic phenocopy in a patient with chronic chagasic cardiomyopathy. Cardiol J 2010; 17: 525–527.Google Scholar
4.Sabatine, MS, Colucci, WS, Schoen, FJ. Primary tumors of the heart. In: Libby P, Bonow RO, Zipes DP, Mann DL (eds). Braunwald's Heart Disease: A Textbook of Cardiovascular Medicine, 7th edn. Saunders, Philadelphia, 2007; 1751.Google Scholar
5.Marx, GR, Flyer, DC. Cardiac tumors. In: Keane JF, Lock JE, Fyler DC (eds). Nadas’ Pediatric Cardiology, 2nd edn. Saunders, Philadelphia, 2006; 825–826.CrossRefGoogle Scholar
6.Amonkar, GP, Kandalkar, BM, Balasubramanian, M. Cardiac rhabdomyoma. Cardiovasc Pathol 2009; 18: 313–314.CrossRefGoogle ScholarPubMed
7.Nakamura, K, Funabashi, N, Miyauchi, H, et al. Hemangioma located just above the left main coronary artery, in a subject who had cardiac arrest due to ventricular fibrillation, led to a diagnosis of Brugada syndrome. Int J Cardiol 2008; 127: 437–441.CrossRefGoogle Scholar
8.Tarin, N, Farre, J, Rubio, JM, Tunon, J, Castro-Dorticos, J. Brugada-like electrocardiographic pattern in a patient with a mediastinal tumor. PACE 1999; 22: 1264–1266.CrossRefGoogle Scholar
9.Junttila, MJ, Gonzalez, M, Lizotte, E, et al. Induced brugada-type electrocardiogram, a sign for imminent malignant arrhythmias. Circulation 2008; 117: 1890–1893.CrossRefGoogle ScholarPubMed