Hostname: page-component-586b7cd67f-l7hp2 Total loading time: 0 Render date: 2024-11-23T17:53:40.112Z Has data issue: false hasContentIssue false

The relationship between scimitar syndrome, so-called scimitar variant, meandering right pulmonary vein, horseshoe lung and pulmonary arterial sling

Published online by Cambridge University Press:  26 May 2006

Shi-Joon Yoo
Affiliation:
Department of Diagnostic Imaging, The Hospital for Sick Children, The University of Toronto Faculty of Medicine, Toronto, Ontario, Canada Division of Cardiology, Department of Pediatrics, The Hospital for Sick Children, The University of Toronto Faculty of Medicine, Toronto, Ontario, Canada
Abdulmajeed Al-Otay
Affiliation:
Division of Cardiology, Department of Pediatrics, The Hospital for Sick Children, The University of Toronto Faculty of Medicine, Toronto, Ontario, Canada
Paul Babyn
Affiliation:
Department of Diagnostic Imaging, The Hospital for Sick Children, The University of Toronto Faculty of Medicine, Toronto, Ontario, Canada

Abstract

We report a case in which a meandering right pulmonary vein connecting to the left atrium is associated with hypoplasia of the right lung, horseshoe lung, abnormal pulmonary lobation, and abnormal branching of the pulmonary arteries. We discuss its relationship to the so-called scimitar variant, and to the scimitar syndrome itself.

Type
Brief Report
Copyright
© 2006 Cambridge University Press

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

Neill CA, Ferencz C, Sabiston DC, Sheldon H. The familial occurrence of hypoplastic right lung with systemic arterial supply and venous drainage “scimitar syndrome”. Bull John Hopkins Hosp 1960; 107: 120.Google Scholar
Morgan JR, Forker AD. Syndrome of hypoplasia of the right lung and dextroposition of the heart: “scimitar sign” with normal pulmonary venous drainage. Circulation 1971; 43: 2730.Google Scholar
Goodman LR, Jamshidi A, Hipona FA. Meandering right pulmonary vein simulating the scimitar syndrome. Chest 1972; 62: 510512.Google Scholar
Pearl W. Scimitar variant. Pediatr Cardiol 1987; 8: 139141.Google Scholar
Mata JM, Castellote A. Pulmonary malformations beyond the neonatal period. In: Lucaya J, Strife JL (eds). Pediatric Chest Imaging: Chest Imaging in Infants and Children. Springer, Berlin, 2002, pp 93111.
Figa FH, Yoo SJ, Burrows PE, Turner-Gomes S, Freedom RM. Horseshoe lung – a case report with unusual bronchial and pleural anomalies and a proposed new classification. Pediatr Radiol 1993; 23: 4447.Google Scholar
Salazar-Mena J, Salazar-Gonzalez J, Salazar-Gonzalez E. Meandering right pulmonary vein: a case of scimitar variant. Pediatr Radiol 1999; 29: 578580.Google Scholar
Agawal PP, Seely JM, Matzinger FR. MDCT of anomalous unilateral single pulmonary vein. Am J Roentgenol 2004; 183: 12411243.Google Scholar
Filho RIR, Cardoso CR, Rossi M. An unusual form of horseshoe lung with hypoplasia of the right pulmonary artery. Int J Cardiol 1991; 31: 259261.Google Scholar
Hwang HK, Chen MR, Chen SJ, Kao HA, Lee KS, Shih SL. Horseshoe lung with pseudo-ring-sling complex. Pediatr Pulmonol 2002; 34: 402404.Google Scholar