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Recanalization and interventional stenting of a closed ductus arteriosus in pulmonary hypertension associated with von Hippel-Lindau disease: a case report

Published online by Cambridge University Press:  14 March 2025

Emine Gülşah Torun Open the ORCID record for Emine Gülşah Torun [Opens in a new window] ,
Denizhan Bağrul Open the ORCID record for Denizhan Bağrul [Opens in a new window]  and
İbrahim Ece
Emine Gülşah Torun*
Affiliation:
Department of Pediatric Cardiology, Ankara Bilkent City Hospital, Ankara, Turkey
Denizhan Bağrul
Affiliation:
Department of Pediatric Cardiology, Ankara Bilkent City Hospital, Ankara, Turkey
İbrahim Ece
Affiliation:
Department of Pediatric Cardiology, Ankara Bilkent City Hospital, Ankara, Turkey
*
Corresponding author: Emine Gülşah Torun; Email: [email protected]
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Abstract

Pulmonary arterial hypertension remains a progressive, life-threatening condition despite advances in medical treatments. We report the first case of the interventional creation of a reverse Potts shunt by stenting a closed ductus arteriosus in a four-year-old child with right ventricular failure due to suprasystemic pulmonary arterial hypertension associated with Von Hippel-Lindau disease, unresponsive to triple anti-pulmonary arterial hypertension therapy. Following the procedure, the patient’s clinical status and echocardiographic systolic and diastolic right ventricular function improved.

Keywords

Pulmonary arterial hypertensionpaediatric interventionreverse Potts shuntvon Hippel-Lindau diseaselocal prostaglandin therapyductal stenting
Type
Brief Report
Information
Cardiology in the Young , First View , pp. 1 - 4
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Copyright
© Emine Gülşah Torun, 2025. Published by Cambridge University Press

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References

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