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Rare case of a superior sinus venosus atrial septal defect presenting with cyanosis

Part of: Cardiac Morphology Atrial Septal Defect (ASD)

Published online by Cambridge University Press:  05 April 2019

Maher Abadeer ,
Michael Luceri  and
Boban Abraham
Maher Abadeer
Affiliation:
Department of Pediatrics, St. Christopher’s Hospital for Children, Philadelphia, Pennsylvania, USA
Michael Luceri
Affiliation:
Department of Cardiology, Nemours Alfred I. duPont Hospital for Children, Wilmington, Delaware, USA
Boban Abraham*
Affiliation:
Department of Cardiology, St. Christopher’s Hospital for Children, Philadelphia, Pennsylvania, USA
*
Author for correspondence: Boban Abraham, MD, St. Christopher’s Hospital for Children, Department of Cardiology, 160 E Erie Ave, Philadelphia, PA 19134, USA. Tel: 215-427-4816; Email: [email protected]
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Abstract

Cyanosis in a newborn is commonly due to intracardiac shunts or duct-dependent lesions. Systemic venous anomalies are uncommon and sinus venous atrial septal defects do not usually present with cyanosis. We report the case of a 4-month-old female with persistent hypoxemia due to a right superior vena cava overriding a superior sinus venous atrial septal defect resulting in a right to left shunt.

Keywords

Anomalous right superior vena cavasuperior sinus venosus defectcyanosis
Type
Brief Report
Information
Cardiology in the Young , Volume 29 , Issue 4 , April 2019 , pp. 544 - 546
Copyright
© Cambridge University Press 2019 

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