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Rare associations of tetralogy of Fallot with anomalous left coronary artery from pulmonary artery and totally anomalous pulmonary venous connection

Published online by Cambridge University Press:  08 April 2016

Supratim Sen ,
Suresh G. Rao  and
Snehal Kulkarni
Supratim Sen*
Affiliation:
Children’s Heart Centre, Kokilaben Dhirubhai Ambani Hospital, Mumbai, India
Suresh G. Rao
Affiliation:
Children’s Heart Centre, Kokilaben Dhirubhai Ambani Hospital, Mumbai, India
Snehal Kulkarni
Affiliation:
Children’s Heart Centre, Kokilaben Dhirubhai Ambani Hospital, Mumbai, India
*
Correspondence to: S. Sen, Children’s Heart Centre, Kokilaben Dhirubhai Ambani Hospital, Four Bunglows, Andheri West, Mumbai 400053, India. Tel: +91 8080329189; Fax: +91 33 23598189; E-mail: [email protected]
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Abstract

We describe the cases of two patients with tetralogy of Fallot, aged 4 years and 8 months, who were incidentally detected to have concomitant anomalous left coronary artery from pulmonary artery and total anomalous pulmonary venous connection, respectively, on preoperative imaging. They underwent surgical correction with good mid-term outcomes. In this study, we discuss the embryological basis, physiological effects, and review the literature of these two unusual associations. Awareness of these rare associations will avoid missed diagnoses and consequent surgical surprises.

Keywords

Tetralogy of Fallottotal anomalous pulmonary venous connectionanomalous left coronary artery from pulmonary arteryunusual associations of tetralogy of Fallot
Type
Brief Reports
Information
Cardiology in the Young , Volume 26 , Issue 5 , June 2016 , pp. 1017 - 1020
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Copyright
© Cambridge University Press 2016 

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