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Rare associations of tetralogy of Fallot with anomalous left coronary artery from pulmonary artery and totally anomalous pulmonary venous connection

Published online by Cambridge University Press:  08 April 2016

Supratim Sen*
Affiliation:
Children’s Heart Centre, Kokilaben Dhirubhai Ambani Hospital, Mumbai, India
Suresh G. Rao
Affiliation:
Children’s Heart Centre, Kokilaben Dhirubhai Ambani Hospital, Mumbai, India
Snehal Kulkarni
Affiliation:
Children’s Heart Centre, Kokilaben Dhirubhai Ambani Hospital, Mumbai, India
*
Correspondence to: S. Sen, Children’s Heart Centre, Kokilaben Dhirubhai Ambani Hospital, Four Bunglows, Andheri West, Mumbai 400053, India. Tel: +91 8080329189; Fax: +91 33 23598189; E-mail: [email protected]

Abstract

We describe the cases of two patients with tetralogy of Fallot, aged 4 years and 8 months, who were incidentally detected to have concomitant anomalous left coronary artery from pulmonary artery and total anomalous pulmonary venous connection, respectively, on preoperative imaging. They underwent surgical correction with good mid-term outcomes. In this study, we discuss the embryological basis, physiological effects, and review the literature of these two unusual associations. Awareness of these rare associations will avoid missed diagnoses and consequent surgical surprises.

Type
Brief Reports
Copyright
© Cambridge University Press 2016 

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