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Pulmonary atresia with intact ventricular septum in the setting of D-transposition of the great arteries associated with hypoplastic left ventricle and severe mitral regurgitation

Part of: Cardiac Morphology

Published online by Cambridge University Press:  28 February 2022

Kota Suzuki Open the ORCID record for Kota Suzuki [Opens in a new window] ,
Norie Mitsushita  and
Akio Ikai
Kota Suzuki*
Affiliation:
Department of Pediatrics, Yamagata University Hospital, Yamagata, Japan
Norie Mitsushita
Affiliation:
Department of Cardiology, Shizuoka Children’s Hospital, Shizuoka, Japan
Akio Ikai
Affiliation:
Department of Cardiac and Thoracic Surgery, Shizuoka Children’s Hospital, Shizuoka, Japan
*
Author for correspondence: K. Suzuki, MD, Department of Pediatrics, Yamagata University Hospital, 2-2-2, Iidanishi, Yamagata-City, Japan. Tel: +81-23-628-5329; Fax: +81-23-628-5332. E-mail: [email protected]
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Abstract

We report the first successful Glenn procedure for pulmonary atresia with intact ventricular septum in the setting of D-transposition of the great arteries. This case was complicated by hypoplastic left ventricle and severe mitral regurgitation. Partial closure of the mitral valve at the time of Blalock-Taussig shunting resulted in improvement of heart failure.

Keywords

D-transpositionpulmonary atresia with intact ventricular septumhypoplastic left ventricleendocardial fibroelastosismitral regurgitation
Type
Brief Report
Information
Cardiology in the Young , Volume 32 , Issue 11 , November 2022 , pp. 1845 - 1847
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Copyright
© The Author(s), 2022. Published by Cambridge University Press

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References

Gupta, SK, Anderson, RH, Kothari, SS. Pulmonary atresia and intact ventricular septum with transposed arterial trunks. Cardiol Young 2015; 25: 161–163.CrossRefGoogle ScholarPubMed
Dayan, JG, Peyvandi, S, Moon-Grady, AJ. Pulmonary atresia with an intact ventricular septum in the setting of D-transposition of the great arteries with a hypoplastic left ventricle: fetal diagnosis. J Ultrasound Med 2015; 34: 2313–2315.CrossRefGoogle ScholarPubMed
Hayes, D, Arya, B, Kleinman, C. Ventriculocoronary fistulae in a patient with transposition of the great arteries, hypoplastic left heart, and pulmonary atresia. Cardiol Young 2013; 23: 111–113.CrossRefGoogle Scholar
Troise, DE, Ranieri, L, Arciprete, PM. Surgical repair for double outlet right ventricle and intact ventricular septum. Ann Thorac Surg 2001; 71: 1018–1019.CrossRefGoogle ScholarPubMed
Napoleone, CP, Formigari, R, Chiappini, B, Frascaroli, G, Gargiulo, G. Surgical management of double outlet right ventricle with intact ventricular septum. Ann Thorac Surg 2003; 75: 586–587.CrossRefGoogle Scholar
Menon, S, Kumar, CJ, Mathew, T, et al. Double outlet right ventricle with intact ventricular septum: avulsion or exclusion. World J Pediatr Congenit Heart Surg 2016; 7: 220–222.CrossRefGoogle ScholarPubMed

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