Hostname: page-component-cd9895bd7-p9bg8 Total loading time: 0 Render date: 2024-12-23T16:05:58.340Z Has data issue: false hasContentIssue false
  • English
  • Français

Pulmonary atresia with intact ventricular septum and antenatal left ventricular failure

Published online by Cambridge University Press:  21 January 2005

Saad Khoshhal ,
George G. S. Sandor  and
Walter J. Duncan
Saad Khoshhal
Affiliation:
Department of Pediatrics, Division of Cardiology, British Columbia Children's Hospital, Vancouver, Canada
George G. S. Sandor
Affiliation:
Department of Pediatrics, Division of Cardiology, British Columbia Children's Hospital, Vancouver, Canada
Walter J. Duncan
Affiliation:
Department of Pediatrics, Division of Cardiology, British Columbia Children's Hospital, Vancouver, Canada
Get access Rights & Permissions [Opens in a new window]

Abstract

Pulmonary atresia with intact ventricular septum has been described extensively, and it is recognized that associated abnormalities of the coronary arteries may cause ischemia. We describe a fetus, diagnosed antenatally as having pulmonary atresia with intact ventricular septum and severe hypoplasia of the right ventricle, who developed severe left ventricular dysfunction. We hypothesize that this is due to reduced coronary blood flow because of falling right ventricular volume in the presence of complete right ventricular coronary arterial dependence.

Keywords

Pulmonary atresiaantenatal left heart failure
Type
Brief Report
Information
Cardiology in the Young , Volume 14 , Issue 3 , June 2004 , pp. 335 - 337
Copyright
© 2004 Cambridge University Press

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

Freedom RM. General morphological considerations. In: Freedom RM (ed.). Pulmonary Atresia with Intact Ventricular Septum. Futura Publishing, Mount Kisco, NY, 1989, pp 17–36.
Daubeney PEF, Delany DJ, Anderson RH, et al., for the United Kingdom and Ireland Collaborative Study of Pulmonary Atresia with Intact Ventricular Septum. Pulmonary atresia with intact ventricular septum: range of morphology in a population-based study. J Am Coll Cardiol 2002; 39: 1670–1679.Google Scholar
Galindo A, Drant SE. Pulmonary atresia with intact ventricular septum. PA-IVS: diagnostic and interventional cardiac catheterization in the neonate. Prog Pediatr Cardiol 2001; 13: 177–182.Google Scholar
Powell AJ, Mayer JE, Lang P, Lock JE. Outcome in infants with pulmonary atresia, intact ventricular septum and right ventricle-dependent coronary circulation. J Am Coll Cardiol 2000; 86: 1272–1274.Google Scholar
Laks H, Plunkett MD. Surgical management of pulmonary atresia with intact ventricular septum. Prog Pediatr Cardiol 2001; 13: 183–197.Google Scholar