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Protein-losing enteropathy in biventricular circulation precipitated by mild stenosis of the inferior caval vein in conjunction with total occlusion of the superior caval vein: a word of caution

Published online by Cambridge University Press:  06 April 2017

Davide Marini ,
Brian A. McCrossan  and
Gabriella Agnoletti
Davide Marini*
Affiliation:
Department of Paediatric Cardiology, Ospedale Infantile Regina Margherita, Città della Salute e della Scienza, Turin, Italy Department of Public Health and Paediatrics, University of Turin, Turin, Italy
Brian A. McCrossan
Affiliation:
Department of Paediatric Cardiology, Royal Belfast Hospital for Sick Children, Belfast, Northern Ireland, UK
Gabriella Agnoletti
Affiliation:
Department of Paediatric Cardiology, Ospedale Infantile Regina Margherita, Città della Salute e della Scienza, Turin, Italy
*
Correspondence to: D. Marini, Department of Paediatric Cardiology, Ospedale Infantile Regina Margherita, Corso Spezia 60, 10126, Torino, Italy. Tel: +39 011 313 5492; Fax: +39 011 313 5482; E-mail: [email protected]
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Abstract

We report the case of a young boy with a history of total occlusion of the superior caval vein, diagnosed early after complex neonatal cardiac surgery, who developed severe protein-losing enteropathy. Protein-losing enteropathy was precipitated by a relatively mild stenosis at the junction of the inferior caval vein with the right atrium. Percutaneous stent dilation of the veno-atrial junction definitively relieved the stenosis, and the protein-losing enteropathy subsequently resolved.

Keywords

Protein-losing enteropathysystemic vein occlusionCT
Type
Brief Report
Information
Cardiology in the Young , Volume 27 , Issue 7 , September 2017 , pp. 1430 - 1433
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Copyright
© Cambridge University Press 2017 

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References

1. Braamskamp, MJ, Dolman, KM, Tabbers, MM. Clinical practice. Protein-losing enteropathy in children. Eur J Pediatr 2010; 169: 1179–1185.Google Scholar
2. Pundi, KN, Johnson, JN, Dearani, JA, et al. 40-year follow-up after the Fontan operation: long-term outcomes of 1,052 patients. J Am Coll Cardiol 2015; 66: 1700–1710.Google Scholar
3. Rychik, J. Protein-losing enteropathy after Fontan operation. Congenit Heart Dis 2007; 2: 288–300.Google Scholar
4. Butera, G, Marini, D, MacDonald, ST. Protein-losing enteropathy resolved by percutaneous intervention. Catheter Cardiovasc Interv 2011; 78: 584–588.Google Scholar
5. Agnoletti, G, Marini, D, Bordese, R, Villar, AM, Gabbarini, F. Interventional catheterization of stenotic or occluded systemic veins in children with or without congenital heart diseases: early results and intermediate follow-up. EuroIntervention 2012; 7: 1317–1325.CrossRefGoogle ScholarPubMed