Hostname: page-component-78c5997874-xbtfd Total loading time: 0 Render date: 2024-11-16T18:24:18.418Z Has data issue: false hasContentIssue false
  • English
  • Français

Normalisation of left ventricular systolic function after change from VVI pacing to biventricular pacing in a child with congenital complete atrioventricular block, long-QT syndrome, and congenital muscular dystrophy: a 10-year follow-up

Published online by Cambridge University Press:  17 May 2013

Sabrina G. Ellesøe ,
Jesper I. Reimers  and
Henrik Ø. Andersen
Sabrina G. Ellesøe*
Affiliation:
Department of Disease Systems Biology, University of Copenhagen, Denmark
Jesper I. Reimers
Affiliation:
Deptartment of Cardiology, Rigshospitalet, Copenhagen, Denmark
Henrik Ø. Andersen
Affiliation:
Deptartment of Cardio Thoracic Surgery, Rigshospitalet, Copenhagen, Denmark
*
Correspondence to: S. G. Ellesøe, Blegdamsvej 3b, lok. 6.2.19, 2200 Copenhagen, Denmark. Tel: 0045 35325039; Fax: 0045 35 32 50 01; E-mail: [email protected]
Get access Rights & Permissions [Opens in a new window]

Abstract

Development of dilated cardiomyopathy in patients with congenital complete atrioventricular block with or without pacemaker is well described. We report a case of dilated cardiomyopathy in a child with congenital complete atrioventricular block, long-QT syndrome, and VVI pacemaker. Temporary pacing in the right ventricular outflow tract demonstrated a 63% increase in cardiac output. After change to biventricular DDD pacing, left ventricular systolic function and diastolic dimensions normalised.

Keywords

Dilated cardiomyopathycongenital complete atrioventricular blockpacemakerbiventricularSmith–Magenis syndromecongenital muscular dystrophy
Type
Brief Reports
Information
Cardiology in the Young , Volume 24 , Issue 3 , June 2014 , pp. 520 - 523
Copyright
Copyright © Cambridge University Press 2013 

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1. Silvetti, MS, Drago, F, Rava, L. Determinants of early dilated cardiomyopathy in neonates with congenital complete atrioventricular block. Europace 2010; 12: 1316–1321.Google Scholar
2. van der Kooi, AJ, de Voogt, WG, Barth, PG, et al. The heart in limb girdle muscular dystrophy. Heart 1998; 79: 73–77.CrossRefGoogle ScholarPubMed
3. Groh, WJ. Arrhythmias in the muscular dystrophies. Heart Rhythm 2012, 30 June (Epub).Google Scholar
4. Edelman, EA, Girirajan, S, Finucane, B, et al. Gender, genotype, and phenotype in Smith-Magenis syndrome: a meta-analysis of 105 cases. Clin Genet 2007; 71: 540–550.Google Scholar
5. Moak, JP, Hasbani, K, Ramwell, C, et al. Dilated cardiomyopathy following right ventricular pacing for AV block in young patients: resolution after upgrading to biventricular pacing systems. J Cardiovasc Electrophysiol 2006; 17: 1068–1071.CrossRefGoogle ScholarPubMed
6. Janousek, J. Cardiac resynchronization in congenital heart disease. Heart 2009; 95: 940–947.Google Scholar
7. Chen, CA, Chang, CI, Wang, JK. Restoration of cardiac function by setting the ventricular pacing at a lower range in an infant with congenital complete atrioventricular block and dilated cardiomyopathy. Int J Cardiol 2008; 131: 38–40.Google Scholar
8. Dubin, AM, Janousek, J, Rhee, E, et al. Resynchronization therapy in pediatric and congenital heart disease patients. J Am Coll Cardiol 2005; 46: 2277–2283.Google Scholar