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Mid-term outcomes of cor triatriatum repair: comparison of biventricular physiology and univentricular physiology

Published online by Cambridge University Press:  10 November 2020

Hiroyuki Nagao*
Affiliation:
Department of Cardiology, Kobe Children’s Hospital, Kobe, Japan
Toshikatsu Tanaka
Affiliation:
Department of Cardiology, Kobe Children’s Hospital, Kobe, Japan
*
Author for correspondence: Hiroyuki Nagao, Department of Cardiology, Kobe Children’s Hospital, 1-6-7 Minatojima-minamimachi, Chuo-ku, Kobe, Hyogo 650-0047, Japan. Tel: +81 078 945 7300. E-mail: [email protected]

Abstract

Background:

Cor triatriatum is the rarest of all congenital cardiac diseases, accounting for 0.1–0.4% of congenital heart diseases. Atrial septal defect is the most common associated defect; however, cor triatriatum is sometimes associated with univentricular heart.

Methods:

This single-centre retrospective study involved all patients who underwent the repair of cor triatriatum at Kobe Children’s Hospital between 2000 and 2020. Twenty-four patients were required surgery. We conducted a survey of survival rate, early and late pulmonary vein stenosis in each group.

Results:

The survival rate of 5 years after cor triatriatum resection was 100% in the biventricular group and 82.1% in the univentricular group, respectively. The free rate for pulmonary stenosis of 5 years after surgery was 100% in the biventricular group and 90.0% in the univentricular group, respectively. There was no statistical difference in survival rate and 5 years free rate for pulmonary stenosis after surgery.

Conclusions:

The results showed that surgical correction offers good early and mid-term outcomes for both cor triatriatum with biventricular and univentricular physiologies.

Type
Original Article
Copyright
© The Author(s), 2020. Published by Cambridge University Press

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